Thanzi, Matenda ndi zokwaniritsa
Gardner syndrome ndi chiyani?
Pali pathologies ambiri anatengera anaika pa mlingo chibadwa. Komabe, ena mwa zimenezi mwamsanga, koma mukadzakula. Ena mwa matenda amenewa Gardner syndrome. kudwala kumeneku kukutanthauza zotupa chosaopsa, nthawi zina ali ndi vuto chotupa chija, mwachitsanzo zipita khansa.
Kufotokozera Gardner syndrome
kudwala uyu ikutchedwa posachedwapa. Choyamba anafotokoza mu m'ma 20, asayansi Gardner. Zinali iye amene anakhazikitsa kugwirizana pakati formations chosaopsa wa khungu, mafupa, ndi kapepala m'mimba. dzina lina la matenda - ndi banja (kapena cholowa) adenomatous polyposis. syndrome Gardner ndi zoopsa osati ochuluka zodzikongoletsera zopindika khungu. Akukhulupirira kuti polyposis m'matumbo amakhala mawonekedwe zilonda mu 90-95% ya milandu. Pachifukwa ichi, ndi kudwala ankaona kuti ziyenera zotupa precancerous. Matenda masiyanidwe ikuchitika ndi atheroma syndrome Riklenghauzena, osteomas limodzi ndi tizilombo ting'onoting'ono matumbo.
The zimayambitsa matenda ndi limagwirira chitukuko
syndrome Gardner amanena kuti ndi kudwala cholowa. Imafalikira chibadwa kwa makolo ndi achibale ake ena (agogo). mtundu wa cholowa cha matenda - autosomal lalikulu. Zimenezi zimatanthauza Mwina mkulu wa kufalitsa matenda ku makolo ndi ana. Pa mtima wa Gardner limagwirira syndrome chitukuko ndi dysplasia mesenchyme. Chifukwa cha nsalu iyi aumbike mwa khungu, fupa ndi mucosa wa mundawo m'mimba, pali khalidwe la matenda chithunzi matenda. Kuwonjezera majini chingawapangitse kukhala zidakwa mesenchymal dysplasia akhoza kupangidwa mchikakamizo cha zinthu zoipa zokhudza chitukuko akalandire chithandizo pa trimester mimba.
syndrome Gardner ndi: zizindikiro
Nthawi zambiri, matenda kumaonekera unyamata (zaka 10). Nthawi zina, zizindikiro chiyamba kenako - kale mu moyo wamkulu. syndrome Gardner ali zotsatira izi: ndi zotupa khungu, zofewa minofu, mafupa ndi dongosolo m'mimba. Kuwonjezera tizilombo ting'onoting'ono m'mimba kumachitika mu m'mimba ndi duodenum. Pa khungu zingaoneke atheroma, dermoid ndi cysts sebaceous, fibroids. N'zothekanso zikamera wa mtima wabwino minofu zofewa. Zikuphatikizapo lipoma ndi leiomyoma. zotupa onsewa angayambe pa nkhope, khungu, manja kapena mapazi. Komanso pali zotupa fupa. Iwo a mtima wabwino, koma zimavuta ntchito. Mwachitsanzo, osteoma fupa la nsagwada m'munsi, chigaza. zophuka izi kusokoneza kutafuna mwina amaumiriza dongosolo ubongo. Mawonetseredwe choopsa cha matenda ndi matumbo ndi tizilombo ting'onoting'ono ndi kapepala zina m'mimba. Nthawi zambiri, zotupa za m'mimba thirakiti mucous nembanemba maligniziruyutsya, mwachitsanzo kuwasandutsa khansa. Tizilombo ting'onoting'ono akhale nthawi yaitali kuti n'komwe. Nthawi zambiri, odwala amadandaula mavuto, matumbo kutsekeka, magazi.
Gardner syndrome chithandizo Cuba: ubwino
Popeza matenda ndi precancer ziyenera ayenera kuchotsa opaleshoni ya zotupa. Nkofunika matenda syndrome Gardner a. Photo odwala Tingaone mu mabuku pa khansara, kapena pa malo apadera. Kuwonjezera mawonetseredwe matenda ndi zofunika kuchita radiography pa mundawo m'mimba, colonoscopy. Khungu zotupa ndi polyposis matumbo kulola matenda zolondola. Gardner syndrome mankhwala ikuchitika m'mayiko ambiri. Ubwino wa zipatala ndi Cuba monga zipangizo zamakono, mtengo wa ntchito opaleshoni, kwambiri akatswiri oyenerera padziko lonse. Mankhwalawa ndi kuchotsa mbali akhudzidwa wa matumbo a. Mukhozanso kuchotsa vuto zodzikongoletsera khungu.
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