Butterfly Syndrome: Bullous Epidermolysis

Bullous epidermolysis (BE), kapena, monga momwe amatchedwanso, matenda a butterfly ndi matenda omwe sakhala obadwa nawo kwambiri. Ana oterewa amatchedwa ana a agulugufe. Ngati muli ndi mayanjano okongola ndi dzina limeneli, ndiye kuti matendawo sali okongola. Ndipotu, odwala omwe ali ndi matenda a epidermolysis amawononga moyo wawo wonse m'masautso owawa. Chifukwa chake ndi khungu lawo, losalimba, ngati mapiko a agulugufe.

Mwatsoka, matendawa "matenda a butterfly" sangathe kuchiritsidwa. Chifukwa zimakhala zovuta kwambiri m'thupi. Ana oterewa amafunikira chisamaliro chapadera: malo abwino kwambiri, zovala ndi nsapato. Ku Russia, matenda osachiritsikawa sakhala nawo m'ndandanda wa matenda osowa kwambiri. Komabe, pali thumba lapadera lothandizira ana a butterfly "Bela".

Chaka chilichonse, ndalama zambiri zimaperekedwa ku thumba ili, kuti athandize ana omwe ali ndi matendawa "butterfly syndrome". Zithunzi za odwala zikhoza kuoneka m'nkhani yathu, komanso mu zolemba za sayansi. Komabe, chidziwitso cha bullous epidermolysis sichinafalitsidwe bwino mu mayiko a Russia ndi CIS.

Matendawa "matenda a butterfly" sakudziwika ndi anthu onse. Ndi ochepa chabe omwe angakhoze kutchula dzina lake lovuta - bullous epidermolysis. Komabe, pali ana otere m'dziko lonse la Russia ndi mayiko a CIS. Odwala onse ali ndi vuto lomwelo: madokotala a kumudzi sakudziwa momwe angachitire ndi iwo, matendawa amatengedwa "ndi diso", osati nthawi zonse zokhudzana ndi matendawa. Ndipo nthawi zina amayi amabisala ana awo, zomwe zimapangitsa kuti aphedwe chifukwa cha chisamaliro chosayenera.

Matenda a gulugufe amadziwika ndi maonekedwe a khungu la munthu. Malingana ndi vesicles, mitundu yotsatira ya bullous epidermolysis (BE) imasiyanitsa:

1. Zosavuta. Amapangidwa pamwamba pa khungu. Khungu limakwera pamitengo ndi mapazi a mapazi. Vesicles akhoza kupanga ngakhale mkamwa.
2. Frontier. Zikuwonekera pa mafananidwe a khungu. Pa matenda aakulu, ma vesicles amatha kuoneka pamakoma a mimba, m'matumbo komanso m'thupi.
3. Dystrophic. Mavalasi amawoneka pamabondo, manja, mabala, mazira, amatha kuyambitsa matenda, amachititsa mavuto kukula ndi zakudya. Mtundu uwu umakhalanso ndi khalidwe la kusanganikirana kwa zala ndi zala.

Matenda a Butterfly ndi chifukwa cholakwika kupanga mapuloteni pakhungu kapena kusakhala kwathunthu. Zomwe zimayambitsa matendawa zimayambitsa matendawa .

Pa kubadwa, khungu la mwana wodwala limakhala ngati khungu la njoka. Zoonadi, izi zimachititsa kuti amayi azichita mantha. Ambiri amangokana ana odwala m'chipatala chakumayi. Koma mwayi wopulumuka mwa mwana yemwe ali ndi matenda oopsya epidermolysis mu malo amasiye ndi pafupifupi zero. Ambiri mwa ana amafa mosasamala. Ndipotu, ana awa amafunika kuchitidwa mosamala kwambiri.

Nthawi yovuta kwambiri kwa odwala ndi zaka zoposa 3. Pakapita pang'onopang'ono, khungu limakhala losalala. Ndipo ana aang'ono, pamene ayesa kukwawa, amachotsa mawondo awo ndi manja awo. Khungu limasungunuka ndipo limachotsa, kupweteka kwambiri. Ana otere sangathe ngakhale kugwirana chanza ngati munthu wamba. Pakukula, pang'onopang'ono amaphunzira kudziteteza okha. Ali ndi zaka zoposa 3, moyo umakhala wosavuta.

Komabe, odwala omwe ali ndi vuto loopsya la epidermolysis amamva kupweteka kwambiri ndi kuyabwa tsiku ndi tsiku, kumene ngakhale antihistamines sathandiza. Kuwonjezera pamenepo, masiku atatu onse ayenera kupirira zofunikira komanso zovala zowawa. Ana otero, monga ena onse odwala, ali apadera. Iwo ali ndi maso osaganiziridwa, mwinamwake kuchokera ku ululu wosasimbika chomwe, chimene ife sitingakhoze kuchimvetsa.