ThanziMatenda ndi zokwaniritsa

Henoch a matenda: pathogenesis, zizindikiro, kudziwika

Hemorrhagic vasculitis (Henoch-Schonlein purpura matenda) limabweretsa anapeza diatheses anachititsa zaphindu kuwonjezeka permeability makoma chotengera. Pali mitundu ingapo ya mawonetseredwe ake. Dzina "Henoch-Schönlein" kupita kudziko lina. Mawu akuti "gemorrragichesky vasculitis" kokha ntchito mankhwala zoweta kuyambira 1959.

matenda Henoch akuti: pathogenesis

Bukuli lili ndi matupi awo sagwirizana kutupa ziwiya ka magazi ndi capillaries. Chifukwa, izo exuded plasma ndi maselo ofiira zili minofu ozungulira. Histopathological zotupa chithunzi ndi pafupi zofanana monga mu periarteritis nodosa. Koma anthu ziwiya zimene kuonongeka mu hemorrhagic vasculitis, ngakhale ang'onoang'ono.

matenda Henoch akuti: zizindikiro

Zingamvekere anthu makamaka achinyamata. Tonga chizindikiro - totupa pa miyendo ndi khalidwe exudative-hemorrhagic. The tinatake tozungulira kungakhale zamitundu yosiyanasiyana, koma ambiri ang'onoang'ono symmetrically mofatsa. totupa nthawi zambiri limodzi ndi molumikizana mafupa, kuyabwa, malaise, ndi kuwuka mu kutentha wonse. Ngati matenda ndi zovuta, ndiye adayala ndi kuphatikiza mu mawanga lalikulu hemorrhagic. Mukhoza kuona magazi kuchokera kufa m'madera ochuluka. masiku 10-15 pambuyo totupa zambiri amaziralira, koma osati kwamuyaya. izo anatchulidwanso pafupipafupi. Chifukwa cha edema periarticular, kusintha mu malo. Nthawi zina matenda Henoch ndi zina zovuta ndi kukha magazi mu zimakhala ndi ziwalo. Ngati kumachitika m'kupita kwa m'mimba ndipo matumbo, m'mimba kuwawa lakuthwa. Kukha mwazi muubongo limodzi ndi chitukuko cha ziwalo ndi paresis. Nthawi zina kusintha zikusonyeza kuti hemorrhagic vasculitis, zimachitika osati ziwalo mkati, ndi mitsempha kwa diso kusintha maso ndi dongosolo chapakati mantha.

matenda Henoch akuti: mawonekedwe

Iwo zinayi: rheumatoid, mphezi-kudya, zosavuta, ndi m'mimba purpura. Aliyense ali ndi zizindikiro zake zenizeni. Zambiri purpura, mwachitsanzo, limodzi ndi totupa hemorrhagic pa khungu ndipo zimagwira ntchito zosiyanasiyana mucous. Aonekera malaise ambiri, kutentha limatuluka. Mu kusintha rheumatoid purpura zimachitika malo (kawirikawiri bondo). Iwo amakhala opweteka kwambiri, pathupi. Ndi wamba a achinyamata ndi ana kumachitika purpura m'mimba. Pamene uka matumbo ndipo m'mimba magazi. Kupweteka kwambiri m'mimba ndi kuukira. Masanzi anati kusakanizikana kwa magazi, dikira chimbudzi. zinthuzo onse limodzi ndi kuwuka mu kutentha thupi. Pa nthawi yomweyo ndi zotupa khalidwe. Pasanathe zambiri iwo patsogolo syndrome m'mimba kapena zimachitika pambuyo. Fulminant purpura ali ndi zizindikiro zomwezo, koma zimakhala zovuta kuti kwa masiku oyambirira angachititse imfa zambiri.

matenda Henoch akuti: kuzindikira

Nkofunika kusiyanitsa izo kwa amapatsira mwana wake ndi thrombocytopenic purpura. Kuvomerezeka zachokera pamaso pa yeniyeni ndi odziwika exudative hemorrhagic zotupa zopweteka olowa ndi matenda ambiri. Poganizira zotsatira za kufufuza ayenera kuganizira chiwerengero cha othandiza magazi kuundana - iwo ali wabwinobwino, palibe kusintha muyenera kukhala zizindikiro za coagulation magazi, psinjika a magazi aumirira.

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