ThanziMatenda ndi zokwaniritsa

Proteus Syndrome: Zizindikiro ndi Njira Chithandizo

Pakali pano, Proteus syndrome imatengedwa ndi chosowa kwambiri majini matenda, amene anatsagana ndi kukula zobwera a mafupa, minofu ndi zimakhala connective. Mwatsoka, matenda ndi mankhwala a matenda amenewa - lovuta kwambiri ndipo sizingatheke ndondomeko.

mankhwala amakono, amadziwika yekha kuti Proteus syndrome ndi matenda otengera ndipo anagwirizana ndi kusintha kwa chibadwa. Komabe, limagwirira kwa pakutchulidwa cha kusintha akadali asanamvetsetse.

Proteus Syndrome: A mbiri pang'ono

Kwa nthawi yoyamba matenda amenewa amanenedwa mu 1979. Ndi pamene Maykl Koen anapeza 200 milandu syndrome ili padziko lonse. Zinali katswiri nampatsa dzina la matenda. Proteus - nyanja mulungu Agiriki. Ndipo, malinga ndi nthano zakale, mulungu izi zikhoza kusintha mawonekedwe ndi kukula kwa thupi lake.

Proteus Syndrome: Zizindikiro

Ndipotu, matenda akhozanso kukopeka ndi zosiyanasiyana kusintha ndi zisokonezo. Monga ulamuliro, ana odwala amabadwa n'kwachibadwa, ndipo kokha ndi zaka za kusintha kuyamba. N'zochititsa chidwi pa nkhani iliyonse, matendawo angakhale osiyana. Odwala ena, matenda majini anatsimikiza mwangozi, popeza palibe zizindikiro kunja simuli pano. Ena odwala M'malo mwake, pafupifupi moyo wake akudwala nkhawa.

Monga tanenera kale, Proteus syndrome (onani chithunzi) limodzi ndi kukula kwa minofu - zingakhale minofu, fupa, khungu lymph ndi mitsempha, mafuta minofu. Zophuka akhoza kuoneka pafupifupi kulikonse. Mwachitsanzo, pali zambiri kuwonjezeka mu kukula kwa mutu ndi miyendo, kusintha mawonekedwe zawo.

Tikumbukenso kuti moyo amayembekezeka anthu yafupika. Komanso sachedwa mavuto ndi mitsempha ya magazi (embolism, thrombosis kwambiri mtsempha), komanso khansa ndi khosi lotupa.

Palokha, Proteus syndrome sayambitsa kakulidwe yomweyo. Koma chifukwa cha overgrowth tima minofu kungakhale zotupa sekondale ya ubongo.

Proteus Syndrome ndi mankhwala ake

Choyamba ndi Dziwani kuti matenda oyambirira ndi zofunika kwambiri. The kale matenda likadziŵika, mpata bwino mwanayo ali ndi moyo wabwino. Monga matenda onse cholowa ndiponso kobadwa nako, vuto si yankho limodzi - n'zosatheka kuchotsa matendawa. Koma njira ya mankhwala amakono kuthetsa zizindikiro zazikulu.

Mwachitsanzo, pamene kukula kwa fupa minofu, kupindika msana, kutalika osiyana ndi manja mwina kuvala zipangizo wapadera mafupa kuthandiza kulimbana ndi vutoli. Ngati matenda amagwirizana ndi kuvutika mu m'thupi kapena chotupa, wodwala ayenera kukhala kuyang'aniridwa zonse dokotala.

Nthawi zambiri ntchito mankhwala opaleshoni. Mwachitsanzo, pogwiritsa ntchito akhoza kukonza kuluma, adzafupikitsidwa mafupa a zala, kuti munthu angathe kugwiritsa ntchito manja onse awiri. Nthawi zina muyenera kukonza fupa ndi minofu connective wa thorax, kuti kuthetsa wodwalayo kuvutika kupuma ndiponso Pomeza.

Mulimonsemo, matenda amafuna chisamaliro nthawi zonse ndi chisamaliro. Njira yokhayo kutalikitsa moyo ndi kusintha khalidwe lake.

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