Ectodermal ndi fibrous dysplasia. impso dysplasia

Pansi dysplasia (anawamasulira kuchokera Greek monga dys - kukana; wplasis - maphunziro) amatanthauza cholakwika ndi kupotoza chitukuko cha chiwalo chilichonse. Izi - liwu gulu kuphimba zakusokonenezedwa.

Fibrous dysplasia amatanthauza matenda a dongosolo chigoba, ndi yodziwika ndi chakuti fupa minofu m'malo ndi minofu fibrous. Zimenezi deforms mafupa. Chifukwa chachikulu cha matenda Maonekedwe a ndondomeko chotupa, limene limayamba pa mwanayo, ndiyeno nkuyamba kupita patsogolo. Fibrous dysplasia zambiri mu akazi.

matenda angapo classifications. Unit ambiri ali, malingana ndi kuchuluka kwa kuchuluka kwa njira pathological:

• monoossalnaya fibrous dysplasia amakhudza yekha fupa limodzi;
• poliossalnaya - n'kusintha anati mafupa angapo (zambiri kufalikira mbali ina ya thupi, ndipo nthawi zambiri amapezeka mu ubwana).

Mawonekedwe woyamba wa matendawa amakhudza fupa cranial, tsamba, mafupa tubular (yaitali) m'mphepete. The chachiwiri - nthawi yomweyo maperesenti oposa makumi asanu a mafupa onse a mafupa a.

Mavuto waukulu monga fractures pafupipafupi, amene mwamsanga coalesce, koma mavuto kuzikonzanso mu mafupa, komanso sarcoma.

Fibrous dysplasia mankhwala aliwonse sangakhale, mungathe njira yokha mafupa (kumuika fupa curettage, osteotomy), ndi kuika mankhwala relieves ululu.

Ectodermal dysplasia limaphatikizapo ambiri matenda ndi syndromes (100), ndicho chimene chiri pamaso pa nthenda chitukuko cha opangidwa kuchokera ectoderm. Chizindikiro choyamba - pamaso pa hyperthermia, chimene anasonyeza, ndiponso kuukira pafupipafupi kungachititse kuti kuswa chitukuko aliyense aluntha, kapena imfa.

Mukhoza kusankha mitundu zotsatirazi ndi zizindikiro zawo.

Angidroticheskaya ayamba kuonekera makanda, mnyamata ndipo akupitiriza moyo. Zinthu zofunika ndi:

• matenda cholowa;
• mapindikidwe amphamvu a mano;
• pamaso pa slowdown mu misomaliyo;
• mucosal manja (kum'mero, m'kamwa, mphuno);
• maonekedwe akunja ndi ofanana odwala mwana ndi kobadwa nako chindoko.

chithandizo Symptomatic wapatsidwa. Ndikoletsedwa: maholide m'mayiko kum'mwera ntchito yotentha ndi mankhwala zomera.

Gidroticheskaya ekzodermalnaya dysplasia amakhala ndi kusintha m'manja, ndi zidendene, tsitsi chitukuko. Monga mankhwala nthawi kutumikiridwa vitamini "A" kunja ndi mkati, olimbikitsa kirimu ndi keratolytics. Kuwonjezera, gwiritsani ntchito: enzymatic zikutanthauza Methyluracilum, anabolic mankhwala, nthaka, amino zidulo ndi biostimulants.

Aimpso dysplasia ali mitundu yambiri zosiyana:

• mawonetseredwe morphological (enaake ndi losavuta);
• Kutanthauzira (cortico-medullary, medullary ndi yokhudza kotekisi);
• kuwanda - okwana segmental, focal).

Chifukwa chachikulu cha matenda ndi majini ndi teratogenic mkati ndi kunja chikoka pa wosabadwayo. Choncho, chifukwa cha matenda ndi kobadwa nako malformations, amene mosaganizira mtundu, kukhala ndi kuchepa mu kukula impso, amwano chitukuko cha parenchyma, kuchepetsa kwambiri ntchito zake.

Kuchiza matenda ndi symptomatic pafupipafupi milandu pamene pali umboni kwa kupatsidwa zina za limba.

Ambiri, dysplasia limapangidwa gulu la matenda omwe Mulungu anawanenanso nthenda chitukuko cha chiwalo kapena dongosolo lonse. Monga ulamuliro, chachikulu amachititsa - majini ndi kobadwa nako.

Mankhwala symptomatic, kapena malangizo ali ndi kumuika chiwalo kapena fupa.