Marfan Syndrome: Amachititsa, Zizindikiro ndi Njira Chithandizo

Marfan syndrome - matenda oopsa, amene kugwirizana ndi kusintha kwa gulu jini yeniyeni. Anthu ndi matenda amenewa amadwala chisokonezo kapangidwe ka minofu connective. Kwa nthawi yoyamba matendawa limafotokonzera 1876 ndi Williams, koma mu 1896, a French dokotala Marfan Kafukufuku mwatsatanetsatane zizindikiro ndi zimene zimayambitsa vutoli ndi kuupereka dzina.

Marfan syndrome: Zoyambitsa

Monga tanenera kale, ndi matenda otengera kwa makolo omwe amagwirizana ndi kusintha kwa majini kabisidwe mapuloteni Ulimbo. Ndi mapuloteni izi ndi udindo kapangidwe yachibadwa minofu connective. Munthu wotere ndi kusintha amabadwa ndi zilema. Komabe, zizindikiro lofotokozeredwa m'njira zosiyanasiyana. Mwachitsanzo, pali odwala amene matenda anatsimikiza mwangozi, popeza palibe kuonekera zizindikiro sanali. Tikawonetsetsa, pali anthu amene akuvutika kwambiri chifukwa cha matenda, chifukwa limodzi ndi deformities misa ndi matenda.

Marfan Syndrome: Zizindikiro

Connective minofu - ndi chofunika kwambiri pafupifupi onse ziwalo ndi kachitidwe mu thupi la munthu. Choncho, Marfan syndrome angasonyeze m'njira zosiyanasiyana - matenda zingakhudze mafupa, minofu, wamanjenje dongosolo ndi mtima:

• Nthawi zambiri, munthu wodwala akhoza kuzindikiridwa ndi kapangidwe ka thupi. Odwala matenda kawirikawiri kwambiri zitani, ndi akanagwiritsa miyendo elongated. Ambiri amadwala zopindika monga kupindika msana, mapazi mosabisa, chisokonezo kapangidwe ka chifuwa.
• syndrome Marfan nthawi zambiri limodzi ndi zotupa za diso - munthu, kusintha kosangalatsa wa magalasi imodzi kapena ziwiri nthawi imodzi. anthu otere adziwa kuti atengeke khungu, mathithi ndi retinal detachment.
• Monga ulamuliro, matenda limodzi ndi anakagumula kapangidwe ndi ntchito dongosolo mtima - makamaka likukwaniritsa chifooke khoma kung'ambika, lomwe ndi loopsa kwambiri kwa moyo.
• Odwala kawirikawiri amakhala ndi zizindikiro Tambasula, ngakhale pambuyo pa mapeto a dongosolo la kukula ndi chitukuko. Komanso, tili pansi pa hernias inguinal ndi ventral.

Marfan syndrome: matenda ndi mankhwala

Pakali pano, palibe mwachindunji matenda njira. Pano kwenikweni muyenera njira mabuku. Kuyamba, dokotala likamva mbiri wangwiro mankhwala, kenako anapereka mayesero ndi maphunziro a machitidwe a minofu ndi mafupa ndi magazi komanso mayeso diso.

Pamene njira ya mankhwala, ndiye ngati matenda ambiri chibadwa, Marfina syndrome amakhalabe ndi munthu kwamuyaya. Koma mothandizidwa ndi njira zamakono mankhwala angathe kuonjezera moyo ndi kuonetsetsa chitonthozo wodwalayo komanso pazinthu. Wodwala ayenera nthawi zonse kuunikira madokotala. Mwachitsanzo, mu nkhani ya mavuto ndi akatswiri masomphenya akhoza perekani kuvala magalasi kapena magalasi. Mothandizidwa ndi mankhwala akhoza kuchotsedwa aliyense zizindikiro za magazi dongosolo, ndi orthotics thandizo yake chitukuko cha mafupa.

Masiku ano, padziko lonse zikukangalika imachitika kafukufuku ku matenda. ndodo Scientific kuyesera kuti adzaone zimene zicitika pamene losokonekera kusintha, ndipo ngati n'zotheka kuti asiye njira kapena mwanjira kusonkhezera izo. Komanso, mankhwala ntchito pa ulimi wa latsopano mankhwala, aluso kuti kungathetse matenda ndi kuthetsa kufala kwa imfa.