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Aplasia - ndi kudwala zimene zingakhudze chiwalo chilichonse

Aplasia - kusonyeza malformations yoopsa, amene anasonyeza sitili mbali iliyonse thupi kapena zigawo minofu. kudwala Ichi ndi kulekanitsidwa kwa hypoplastic pa thupi akhale wakhanda kapena yafupika kukula ndi ufulu dongosolo yachibadwa.

Ichi ndi chifukwa chake pali kudwala

Tikumbukenso kuti aplasia - matenda obadwa kuti kumachitika chifukwa cha zimakhudza mwana wosabadwayo mwachindunji kapena mwa njira zina mwa thupi la mayi wa thupi, mankhwala ndi zifukwa za chilengedwe. Iwo, wotumidwa gametes makolo kapena makolo awo, zimatha kupundula chromosomal ndi kusapezeka kwa chiwalo kapena minofu.

Mwa njira, ndi chimanga chosakhwima wina limba mu Ndisanaumbidwe ndi pafupifupi wakutali atsogolera zambiri imfa kugwirizana thupi ena. Mwachitsanzo, mu pakalibe Mphukira ureteric amapezeka sekondale aimpso aplasia, ndi mamita P..

A tsiku odulidwa wolemera, kenako zopindika amafotokozedwa Ndisanaumbidwe ndi sangathenso kukhala, - ichi ndi mwezi woyamba wa moyo intrauterine.

Features la mapangidwe kudwala

palibe malo amene sakhoza anati aplasia anthu. Izi boma pathological mmodzi wa ziwalo wophatikizidwa ambiri amachititsa hypertrophy wina (aplasia imodzi zopangitsa za endocrine zikhoza hypertrophy ena). Choncho, pali m'malo, chipukuta misozi ntchito anataya.

Nthawi zambiri palibe mbali ya thupi, monga aplasia wa ku corpus callosum kapena ubongo olfactory (a chikhalidwe wotchedwa arinentsefaliey), etc. Aplasia minofu ndi kawirikawiri pa khungu la. Pa mfundo imeneyi wakhanda wabadwa wapezeka chilema, zomwe kawirikawiri sakhala upambana masentimita 5. Koma ngati boma zimagwira Chilwa zakuya, mwachitsanzo monga ulamuliro, minofu aplasia, mu nkhani ya embryonic slits chitsegukire (T. N. Dizarfiya).

Nthenda chitukuko cha minofu fupa

Monga milandu tafotokozazi, aplasia fupa mawonekedwe akutali ali osowa kwambiri. Choncho, pamene matenda amenewa mu nthambi mtima fibula adzafupikitsidwa akufotokozera equinovarus phazi chilema (m'mphepete kutsogolo nthawi yomweyo aukitsidwa, ndi akunja - zasiyidwa), yokhota kumapeto tibia, palibe ng'ombe ndi minofu peroneal.

Aplasia milandu munthu olembedwa mankhwala ziwalo, nthawi zambiri zimachitika ndi miyendo anthu. Zimenezi zingakhale kupanda zala kapena zambiri kapena dzanja lonse kapena phazi. Pafupipafupi kupanda options kwa mkono, atavalanso zoteteza, phewa, ntchafu, pamaso pa phazi kapena dzanja.

Aplasia a chigaza ndi ubongo

Pamene focal aplasia mafupa Chigaza, amene mankhwala amatchedwanso "fenestrated chigaza", izo anapanga kudzera zopindika ndi kukula osiyana ndi mawonekedwe. Koma periosteum (Kakhungu fibrous kuphimba fupa) ndi khungu pa malo vuto ilipobe. Iwo zili makamaka mu parietal ndi mazunzo zigawo.

Ngati wakhanda mafupa a Chigaza, ndi zambiri nawo kumeneko mafuta aplasia (Limatchedwanso anencephaly). kudwala Izi 100% amapha. Komanso, 75% ya ana kufa mu utero, ndipo wotsalawo moyo kuposa masiku 5 atabadwa.

Ngakhale kudziwika nkhani ya kubadwa mu United States mu 1992, mtsikana matenda amenewa, amene anakhalako zaka 2 ndi masiku 174. Kupuma ndi kugwira ntchito kwa ziwalo mthupi lake zinachitikadi ndi osungidwa ubongo tsinde. Koma, koma, mtsikana nthawi chikugwirizana ndi makina komanso mavuto akutulukira kuyambitsa amasiya ake.

Aplasia la chiberekero ndi nyini

Milandu underdevelopment kapena kusapezeka kwa chiberekero, Ukalawu ndi nyini - kawirikawiri anakumana chosayenerera. Akazi amene ali, akhoza sanaime kapena mwana wako yemwe.

vuto wapezeka ndi zambiri kale kufika msinkhu. Kwa dokotala Woman kubweretsa madandaulo za kusowa kusamba ndi (pakalibe nyini), ndikosatheka moyo kugonana. Pankhaniyi, wodwalayo zambiri anakhalabe yachibadwa thupi kapangidwe ndi bwino anayamba sekondale makhalidwe kugonana.

Ngati wodwalayo tsankho aplasia kumaliseche, izo angadandaule za mwezi magazi m'mphuno, chifuwa mwachikondi, ndi zowawa zojambula pamimba m'munsi, amene anatsagana ndi kudzikundikira otaya kusamba, kuyambira outflow pamene matenda sangapatsidwe dzina.

Chotero chodabwitsa ndi kumabweretsa formations chotupa - otchedwa hematocolpos. Akamakula m'munsi m'mimba ululu arching kuoneka lakuthwa, pamene suppuration waikamo precipitates auka kutentha, kulenga zinthu yabwino kwa sepsis. Wodwala mu nkhani iyi ikusonyeza opareshoni mwamsanga.

Pamene zotupa la chiberekero si njira, popeza palibe thupi, kumasuka magazi.

Aplasia - si nthawi zonse aphedwa

Zotsatira pa thupi aplasia ziwalo zosiyanasiyana, zimakhala kapena ziwalo ndi osiyana. Mitundu ina ya aplasia (pakalibe hemispheres oziziritsa, minofu mtima, impso ziwiri, ndi zina zotero. N.) Kodi atakwatirana ndi moyo. Ena zingachititse kukanika choopsa cha thupi, ndipo palibe opaleshoni kungachititse kuti imfa ya mtima (diaphragmatic chophukacho , kapena matenda Hirschsprung).

Koma sitili pa gawo kapena onse chiwalo, komanso aplasia la chiberekero, izo n'zogwirizana ndi moyo. A awiri umodzi wa thupi chimanga chosakhwima, monga aplasia unilateral aimpso, nthawi zina kwathunthu kulipidwa hypertrophy wa mnzake, mukatero akhoza kukomoka kuonekera pa moyo wodwalayo.

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