ThanziMatenda ndi zokwaniritsa

Cholowa matenda - enaake fibrosis: zizindikiro ndi kuwonekera kwa matenda

Enaake fibrosis ndi matenda otengera chifukwa cha jini mutated amakhala ndi zotupa za kapamba, zovuta matenda zinchito ziwalo kupuma ndi kapepala m'mimba.
Pa mtima wa matenda enaake fibrosis amene matenda wapangidwa ali wamng'ono ndi wa kusintha kwa maselo. matenda amapezeka mwana mmodzi wa zikwi ziwiri, pafupifupi magawo atatu a milandu kufa pamaso pa zaka makumi atatu. Ngati makolo onse apeza jini mutated, chiopsezo ndi mwana ndi ukuwonjezeka matendawa kwa 25%. Childs, onyamula nthenda jini sikuti amadwala enaake fibrosis.

Pa ana akhanda amene amapezeka ndi zizindikiro enaake fibrosis mu masiku oyambirira. About wachitatu anabadwa pali meconium ileus, chifukwa mu blockage wa dera wapotalikira ina yaing'ono intestine viscous wakuda meconium. Ndi tsiku lachiwiri atabadwa ana odwala kukhala wosakhazikika, zidzachitika bloating, kusanza kapena regurgitation a zolemba. Patapita masiku angapo chikhalidwe mwana worsens chifukwa cha kuchuluka kwa kuledzera. Pamene kutsekeka akuyamba mavuto a meconium peritonitis ndi matumbo perforation.
Komanso, pali chifuwa chosatherapo, kuyan'anila za mpando, ana kwanthawi kumbuyo mu ndege thupi - zonse zimenezi zimachititsa enaake fibrosis. Zizindikiro akhoza kugonjetsa mzake. Mwachitsanzo, chifuwa ndi amaonera maonekedwe a matenda chapamwamba kupuma thirakiti. Pachiyambi ndi youma komanso yosowa, ndiye m'kati ndipo aakulu. Chifukwa, kutsokomola kusalima kuyamba kuutsa kusanza.

Odwala amene anapulumutsa enaake fibrosis, zizindikiro ndi pafupipafupi mvula chonunkha chopondapo, ndi ochititsa zotsalira undigested chakudya. Fecal zovuta muzimutsuka kuchokera mchikuta kapena mphika, pamaso zosafunika mwina kuonekera mafuta. Odwala ena zidzagwa kuchokera rectum.
Mu 70 peresenti milandu matenda anatsimikiza mu zaka 2 moyo. Pa zaka sukulu chizindikiritso cha enaake fibrosis kugwirizana ndi mawonekedwe wofatsa wa kusintha ndi kuteteza kapamba. Mu akula, milandu matenda enaake fibrosis, zizindikiro angapezeke kawirikawiri, pokha pokha atypical matenda.

Lero, kuti amuchotsepo anomaly si zotheka. Odwala ndi matenda a enaake fibrosis chithandizo nthawi zonse samalani zonse moyo wautali. Ndipo mwamsanga matenda anapangidwa, chithandizocho anayamba kwambiri, chitsimikizo kuti wodwalayo bwino. Zachitika pa mankhwala a matenda zimene zayambitsa kuti kulola akazi ndi matenda zoopsa kufika msinkhu wobereka. Samalira mlingo kupulumuka.
Odwala enaake fibrosis pamoyo wawo ziri zofunika Mlingo lalikulu kumwa mankhwala kuti wawononga ntchofu ndi zimakhudzidwa kulekana ndi. Kukula ndi chitukuko cha ana amayamba kupesa kukonzekera, mwinamwake chakudya simudzapezeka odzipereka. Iyo imayimba yofunika zakudya zabwino. Kulamulira matenda a dongosolo kupuma, chifukwa mpumulo ndi kuteteza zofuna muyambirenso mankhwala. Ngati ndili enaake fibrosis, zizindikiro za amene afotokozedwa mu zotupa chiwindi, kwa chiwindi muyenera kudya zonse, amene bwino ntchito ya maselo chiwindi ndi woonda magazi.

Pamene chithandizocho ayenera kutsatira zakudya zapadera, zili chimene kuchuluka ndalama zomanga thupi, mafuta ndi kupezeka zimam'patsa zogwirizana ndi m'badwo. Anamuika mavitamini. ana odwala inayenera kukhala kuyang'aniridwa ndi dokotala. Ngati matenda si patsogolo m'chipatala si chofunika. M'munda wa ana odwala ali osavomerezeka pa galimoto, sukulu bungwe ulamuliro wapadera kwa iwo.

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