Thanzi, Matenda ndi zokwaniritsa
Gilbert ndi matenda. matenda ake, zotsatira
syndrome Gilbert, ndi matendawa? Gilbert ndi matenda - kwambiri wofatsa matenda zosinthika zinchito hyperbilirubinemia. matenda limasonyeza UGT1A1 jini kusintha. Chifukwa cha iye, enzyme ndi ndiyotengera ndi UDP. syndrome Gilbert a amakhala ndi zotsatirazi:
- misinkhu apamwamba bilurbina magazi
- Tsankho kulephera glyukuroniltransferazy
- Pakalibe kusintha kwa chiwindi
- Kuchepetsa bilirubin okwera chifukwa kanthu ya phenobarbital
Kwa nthawi yoyamba syndrome Gilbert a anapezeka mu 1901, French madokotala Gilbert Nicolas Augustin ndi Lereboullet P. anazindikira vuto ngati "cholehemia banja". Kenako, adapempha maina owerengeka, koma anasiya pa matenda Gilbert a. syndrome kawirikawiri amapezeka amuna zaka 25-30.
Zizindikiro mmene matenda
Anthu, pali kutopa, pomwe chapamwamba nusu colic zimachitika. Chiwonetsero chachikulu cha matendawa ndi nkhawa ndi mtundu utoto. Nthawi zina zimachitika kuti yellowness si noticeable, ndipo munthu amaphunzira za matenda pokhapo msonkhano amuzolengedwa chamoyo. Pali mitundu iwiri ya matenda: episodic ndi aakulu. Ngati munthu mwakuthupi overloading thupi lanulo, matenda a chikasu ndiyo angagwe. Komanso, uchidakwa, njala angakhale "kuyamba" pa chitukuko cha matenda.
Gilbert ndi matenda matenda.
Cacikulu bilubirin pa matenda angakhale pa mlingo wa 21-51 mmol / l, mmene n'zotheka kuonjezera mlingo wa 85-130 micromoles / lita. Kudziwa matenda, muyenera anadutsa matenda wapadera. Iwo akhoza kukhala a mitundu yosiyanasiyana.
- Mayeso ndi njala. Zimagwiritsa ntchito otsika-mafuta zakudya, osachepera - kusala kudya kwa maola 48. Motero anthu ambiri bilirubin mu ukuwonjezeka magazi.
- Mayeso pentobarbital. Kugwiritsa ntchito mankhwala kumabweretsa kukondoweza za ntchito enzyme glyukuroniltrasferazu, potero kuchepetsa mlingo wa bilirubin.
mankhwala a matenda
Aliyense chithandizo chapadera, ambiri, ayi, chifukwa ndi mbali ya chamoyo, osati matenda. Monga kudwala contraindicated owonjezera katundu, ayenera kutsatira zakudya zapadera. mowa munthu ziyenera oletsedwa chifukwa ntchito zawo kungachititse kuti chitukuko cha matenda. Koma M'pofunikanso kukumbukira kuti milandu syndrome Gilbert sikofunika kukana vaccinations. Pa amveke matenda a chikasu ndiyo madokotala mankhwala ndi zakudya zina, vitamini mankhwala Kwalamulidwa.
Gilbert ndi zotsatira syndrome
Amene anapeza syndrome Gilbert ndi zotsatira za chidwi, komanso mmene matenda zidzakhudza chiwindi. Ena zotsatira sangakhale konse, koma ndi bwino kuchita ultrasound a chiwindi, komanso magazi kuti bilirubin. Kwa chiwindi anakhalabe labwinobwino pa kudziwika syndrome Gilbert muyenela kumamatira kwa zakudya, ndi kuchepetsa nokha kuti uzichita. Nthawi zina zotsatira za matenda angasonyeze chosakhalitsa pigment steatosis. Kwenikweni, zotsatira izi anati anthu. Choncho, anthu amene akudwala matendawa ayenera kuwunika thanzi lawo.
ndi Zoneneratu kuika odwala chiyani?
matenda tinganene kuti ndi zosinthika ya mwakale. anthu amenewa amaonedwa kuti ndi wathanzi, makamaka pa matenda wapadera iwo safuna. Ngakhale kuti hyperbilirubinemia akhoza anakhalabe moyo, syndrome Gilbert alibe ndi imfa. Pali kuthekera kwa matenda obwera chifukwa choganiza kwambiri, ndipo cholelithiasis. Zotsatira za matenda mwina kudzaonekera zaka 20, koma nthawi zonse limodzi ndi munthu, kwambiri kuti akhoza kuchita chibadwa china. Chinthu chofunika kwambiri ndi matenda alibe zimakhudzira pa zochita za anthu.
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