Enaake fibrosis ndi mwana: zizindikiro, zizindikiro, chithandizo

Mmodzi wa matenda ambiri ambiri amene tinabadwa ndi enaake fibrosis. The mwana amapangidwa ndi chinsinsi tizilombo kuti kumabweretsa kusokonezeka kwa thirakiti m'mimba, dongosolo kupuma. Characteristically, matenda ndi okhalitsa ndipo kawirikawiri kumaonekera, ngati makolo anu onse ali ina zosalongosoka mbewu. Ngati malo ndi kusintha imodzi yokha ya makolo, ana sadzalowa matenda. Kawirikawiri, enaake fibrosis amawapeza mu chaka choyamba cha moyo (kapena m'mimba).

Mbiri ya matenda

Enaake fibrosis ana akufotokozera chifukwa kusokoneza kapangidwe ka khromozomu 7 (phewa lake). Mu nkhani iyi, ntchofu mu thupi umakhala viscous. Amadziwika kuti chinsinsi cha mtundu okutidwa ndi pafupifupi onse ziwalo. Chifukwa pamwamba yothira iwo, ndipo patukani, ntchofu owonjezera aisadza iyo. Koma ngati zichitika kuti osaitanidwa, ndi katulutsidwe viscous stagnates amasonkhana. M'madera oterewa, ndi tizilombo toyambitsa matenda kuchulukana, zikubweretsa matenda okhazikika. Kenako anakhudzidwa ziwalo dongosolo m'mimba, ndi chamoyo amadwala kupanda oxygen. Kwa nthawi yoyamba pa mwana enaake fibrosis limafotokonzera 1938 ndi D. Anderson. Mpaka nthawi imeneyo, ambiri ana amafa chibayo ndi matenda ena amene amayamba chifukwa enaake fibrosis. Zambiri zokhudza matenda anatuluka mu mzaka zana makumi awiri mochedwa. Pafupifupi makumi awiri wokhala lathuli - chotengera cha enaake mutating fibrosis mbewu. chilema Izi sizikugwirizana ndi zizolowezi zoipa za makolo pa mimba, ndi mankhwala osokoneza bongo. Komanso pa kukhalapo kwake si bwanji akumane zinthu zachilengedwe. Akudwala yemweyo anyamata ndi atsikana.

mawonekedwe a enaake fibrosis

Matendawa akhoza kukhala akalumikidzidwa zitatu.

• Woyamba - m'mapapo. Zimachitika pafupifupi 15-20% ya chiwerengero cha milandu onse. Yodziwika ndi chakuti bronchi kukhala mutadzala ntchofu wandiweyani. Patapita nthawi, iwo amatha yatsekera kwathunthu. Chinsinsi wokhala kwambiri kuswana pansi tizilombo toyambitsa. M'kupita kwa nthawi, m'mapapo minofu losindikizidwa, timauma. Cysts kuonekera. ntchito mopitirira ndi m'mapapo mwanga chatsitsa yekha. Munthu akhoza kufa chifukwa suffocation.
• Enaake fibrosis, mwana akhoza kukhala ndi mtundu matumbo. Mu ichi akusokoneza dongosolo m'mimba, zakudya ndi bwino digested. makhalidwe amenewa amachititsa chitukuko cha matenda a shuga, chironda chachikulu, chiwindi matenda enaake ndi zina zotero. N. Umapezeka 5% ya milandu.
• Ambiri mtundu - osokonezeka. Iwo amawapeza mu 75% ya odwala matenda chibadwa.
• chosowa kwambiri (1%) akupezeka, ndi maonekedwe atypical.

Enaake fibrosis a m'mapapo ana

mawonekedwe nthendayo zambiri amatchedwa kupuma lapansi. Kawirikawiri, zizindikiro ndi akuwonetseredwa mu akhanda yomweyo. Enaake fibrosis a m'mapapo ana ali ndi zizindikiro ngati chifuwa, kufooka ambiri, wotumbululuka khungu. M'kupita kwa nthawi, kuzikonzanso chifuwa, izo limodzi ndi kutulutsidwa kwa ntchofu wandiweyani. Wosweka njira mpweya kutengerapo. Kodi thicken nsonga zala. Nthawi zambiri ana ndi enaake fibrosis, ndipo akudwala chibayo, lomwe limapezeka mu mwachilungamo kwambiri. minofu kupuma anakhudzidwa purulent kutupa. Chibayo amakhala aakulu. Mwina kuchuluka kwa minofu connective mu mapapo. M'kupita kwa nthawi, pali milandu maonekedwe a "mtima m'mapapo mwanga".

M'mapapo mwanga enaake zizindikiro fibrosis ana ndi akulu ndi ofanana: zemlyanistogo khungu, chifuwa afika bochkopodobnuyu kuumba mosavuta olumala. Komanso, pali kufupika kwa mpweya ngakhale pa mpumulo. Chifukwa kuchepetsa njala ndi kuchepetsedwa kulemera kwa wodwalayo. Komabe, zizindikiro akhoza kuoneka patapita nthawi yaitali. Izi - mawonekedwe abwino kwambiri wodwalayo.

Gawo enaake fibrosis otaya m'mapapo

Pali magawo angapo a Inde matenda.

1. Gawo loyamba amakhala ndi maonekedwe a chifuwa, zambiri youma ndi wopanda sputum. ndi kupuma movutikira kumachitika zina. Mbali yapadera ya siteji iyi kuti ukhoza ngakhale zaka zingapo (10).
2. Gawo lachiwiri - ndi zikamera chifuwa mu mawonekedwe aakulu, kusintha phalanges lapansi. Kupezeka Kugawilidwa kwanthaka kukhosomola. digiri Izi matenda komanso kumatenga ndithu nthawi yaitali - mpaka zaka 15.
3. Mu gawo lachitatu mavuto kukhala. Zachepetsedwa m'mapapo minofu, cysts kuonekera. Against maziko awa, ndi kuvutika ndi mtima. Kutalika kwa nthawi ya matenda - zaka 3-5.
4. Mbali wachinayi (a miyezi ingapo) amakhala ndi kugonjetsa lolemera kwambiri ya dongosolo kupuma, mtima. Zotsatira zake zimakhala zambiri amapha.

Zizindikiro za m'mimba enaake fibrosis

Izi mawonekedwe a matenda yodziwika ndi kulephera mu dongosolo m'mimba. Matumbo enaake fibrosis mwana momveka bwino kumaonekera mu nthawi ya atasiya kuyamwa. Pankhaniyi, pali osauka mayamwidwe mafuta, mapuloteni (chakudya ali m'mimba pang'ono bwino). Chifukwa chitukuko cha njira ya kuvunda m'matumbo anapanga mankhwala akupha, amawonjezereka m'mimba. A nambala yaikulu kayendedwe matumbo kumawonjezera. Ngati anapezeka ndi "enaake fibrosis" (enteric mawonekedwe) ana akhozanso thumbo prolapse. Nthawi zambiri odwala amadandaula pakamwa youma. Utrudnyaetsya kulandira chakudya youma. Ndi kupitirira zina matendawa yafupika thupi.

Matendawa komanso yodziwika polyhypovitaminosis kuyambira chifukwa mavuto chimbudzi thupi silingathe mavitamini pafupifupi magulu onse. Monga ulamuliro, minofu kutaya kamvekedwe awo, khungu kumakhala kosavuta zotanuka. Mmodzi zambiri zizindikiro khalidwe la enaake fibrosis ana (matumbo mtundu) - kupweteka kwa chikhalidwe chosiyana pa pamimba. M'kupita kwa nthawi, kungakhale ndi chironda chachikulu matenda, ndi matenda a shuga (zobisika mawonekedwe). matendawa amakhudza impso, chiwindi. Ngati chidwi ndi chiwindi, mpando amakhala akuda. Poizoni anapeza mu thupi ndi kukwaniritsa m'magazi ku ubongo. Iwo ndi zotsatira zoipa maselo mitsempha, kukhala encephalopathy. Kumathandiza zichuluke pang'onopang'ono ndulu matumbo enaake fibrosis ana. Photography pathologically asintha matumbo (mu gawo mtanda) chili m'munsimu.

Obwerawa mawonekedwe a matenda

Mtundu wa matenda amakhala ndi zizindikiro za onse inhalational ndi matumbo. Childs, akhanda anati pafupipafupi ndiponso yaitali chibayo, chifuwa. Pafupifupi onse milandu, ndi chifuwa alipo. Komanso, wosakaniza enaake fibrosis ana limodzi ndi bloating, chopondapo nthawi zambiri madzi, mtundu wake ukusandulika wobiriwira. Pali malumikizanidwe cha kukula kwa matenda kuchokera pamene zizindikiro za poyamba. Nthawi zambiri, ngati zizindikiro yoyamba wapezeka ali aang'ono, kuti madokotala ananena zawo ndi akumane ndithu.

meconium ileus

Enaake fibrosis amakwiya kuwonjezeka kukhuthala zinsinsi chamoyo, kuphatikizapo meconium - chopondapo choyambirira ana. Zimenezi zimachititsa blockage ndi intestine. Izi mawonekedwe a matenda limapezeka pa kubadwa pamene meconium Kodi zisachoke. Mwana amakhala wosakhazikika, nthawi zambiri regurgitates (ngakhale ndi zosafunika ya ndulu). Komanso pali bloating, khungu amakhala wotumbululuka. matenda Komanso otaya amathandiza kuonetsetsa kuti akhanda kwambiri kumachepetsa injini ntchito (ngati sichoncho mabasi). Chifukwa chikhalidwe ichi ndi pakalibe trypsin. Meconium ileus ndi woopsa kwambiri ndipo amafuna alowererepo pa opaleshoni.

matenda a matenda

Matenda a enaake fibrosis ana zikuphatikizapo mosamala kwa kuvutika cholowa ndiponso kobadwa nako. Komanso, magazi, mkodzo ndi sputum kumaliseche. Mawaya ndi coprogram. Timatha kudziwa pamaso pa inclusions mafuta mu ndowe za mwanayo. Anafufuza kupuma system (radiography, bronchography, bronchoscopy). Koyenera ndipo spirometry, monga timatha kupenda boma la mapapo zinchito. Ngati mukukayikira kuti munthu enaake fibrosis (zizindikiro ana mwina kuonekera) kafukufuku chibadwa. Iwo kuthandiza kukhazikitsa pamaso pa kusintha jini kuti ndi udindo ntchito secretory wa chamoyo. Neonatal neonatal mosamala imagwiridwa (trypsin ndende ndi ankafufuza mu zouma magazi banga). Ndi nkhani zokwanira ndi mayeso thukuta. Ngati mphika anaulula ayoni sodium, chlorine mu kuchuluka kuchuluka, n'zotheka kulankhula kuli matenda ndi Mwina mkulu. Ngati mkazi amene banja anthu ndi matenda a "enaake fibrosis", akuyembekezera mwana, madokotala analimbikitsa tione madzimadzi amniotic pa zaka pafupifupi 18-20 masabata.

mankhwala enaake fibrosis

Dziwani kuti tichotse matenda ndi zosatheka. Komabe, mankhwala akhoza kwambiri kuwongolera moyo ndi nthawi yake. Poyamba, odwala ambiri ndi matenda ofanana kufa pamaso pa zaka 20. Koma tsopano, ndi mankhwalawa yake akhoza moyo kwambiri yaitali. mawonekedwe matumbo amafuna zakudya zapadera. Chakudya ayenera kukhala wolemera mu mapuloteni (nsomba, mazira). Komanso zoikika ndi mavitamini zovuta. Kunatanthauzanso phwando michere ( "Creon", "pantsitrat", "zoikidwa" neri Al.). Dziwani kuti mankhwala ayenera kumwedwa pa moyo wake. chakuti mankhwala amapereka zotsatira adzasonyeza normalization wa chopondapo, kuwonda komanso kusowa ngakhale kukula. ululu m'mimba kutha, ndi ndowe si wapezeka kulolerana wa mafuta.

Pamene m'mapapo mwanga mawonekedwe mankhwala a matenda ndi zofunika kuti atsogolere liquefaction wa sputum ndi bronchial kubwezeretsa magwiridwe ( "Mukosolvin", "Mukaltin"). Nkofunika mankhwalawa m'mapapo mwanga enaake fibrosis kupewa chitukuko cha njira opatsirana mu mapapo. umapangitsa ndi wapadera kupuma kokoka. Izo zizichitidwa zonse. Kuchipatalako angathe kuperekedwa ndi mankhwala. Iwalani za matenda kwa nthawi ndithu kuthandiza ngati njira kwakukulu, ngati kupatsidwa zina za m'mapapo. Komabe, iwo ali ndi zovuta zake: chiopsezo kukanidwa, utsogoleli wa mankhwala ziletsa chitetezo cha m'thupi. Komanso, wodwala ayenera kukhala mu chikhalidwe chake labwino. Ambiri kupatsa izi anachita kunja.

Ayamikira anapanga odwala enaake fibrosis

Madokotala mwamphamvu amalangiza kuti odwala matenda izi kuti vaccinations yake ndi chifuwa akuphokosera, ndi matenda ofanana. Nkofunika kuthetsa allergens angathe: Pet dander, mapilo mabulangete kwa mbalame nthenga. Amagwiritsidwanso koletsedwa kwa chabe kusuta. Chotero matenda kumafuna spa mankhwala a ana. Ngati mlingo wa kukula kwa matenda si yovuta, mwana kusukulu, zibonga masewera, ali ndi moyo mwachilungamo yogwira. Chithandizo cha enaake fibrosis ana azaka pansi chaka chimodzi zimaphatikizapo kugwiritsa ntchito zosakaniza wapadera (Dietta Owonjezera, Dietta Plus). Komanso, kufunika Kuonjezera ndi mlingo umodzi wa nthawi 1.5. Komanso anadzetsa zakudya mwanayo ndi pang'ono mchere (ichi n'kofunika m'chilimwe).

mwapadera ayenera kukhala menyu mtima. Ziyenera kukhala zamafuta (kirimu, batala, nyama) monga mayamwidwe wa zakudya wosweka. Kumwa amafunika zambiri. M'pofunikanso kukumbukira kuti kutenga kukonzekera enzyme chofunika tsiku. Kuwonjezera chithandizo zoyamba angagwiritsidwe ntchito ndi mankhwala azitsamba. Facilitates expectoration zitsamba monga marshmallow, mayi ndi akulera ana opeza. umapangitsa dongosolo m'mimba ndi dandelion, elecampane. Ndipo mafuta zofunika ntchito inhalations (lavender, Basil, kamtengo ka hisope). Kumathandiza ndi kumanga zinthu monga uchi.

Zoneneratu

Mwatsoka, moyo amayembekezeka kwa matenda anapatsidwa si kwambiri. Pafupifupi odwala moyo zaka pafupifupi 30 (mu Russia), kapena mpaka 40 kapena kuposa (kunja). Komabe, panthawi yake matenda ndi mankhwalawa kwambiri kusintha mmene alili. Kwambiri akumane madokotala ananena zawo - mu maonekedwe oyambirira enaake fibrosis (makanda). Koma amadziwika ndi mlandu pamene wodwala matenda ofanana anakhala zaka zoposa 70. Kusiyana mu moyo amayembekezeka Russia ndi mayiko ena chifukwa mbali ndalama. odwala kunja kulandira thandizo moyo wautali wa boma. Chifukwa ichi iwo akhoza munthu wabwinobwino, kuphunzira, kulenga banja ndipo ali ndi ana. Koma Russia akhoza mokwanira kupereka odwala mankhwala zofunika (ndi kukonzekera izi enzyme, ndi mankhwala apadera, ndipo mucolytics). Only owerengeka ana akalandire chithandizo ufulu mankhwala ndi mankhwala kutero. Odwala kukhala mu nkhani yapadera ya moyo wake wonse. Kuti achotse pakutchulidwa zoterozo matenda ayenera kuonana ndi zachibadwa pa siteji ina ya mapulani mimba.

nsonga maganizo kwa makolo

A zambiri mabuku kuti athandizire makolo amene mwana amadwala enaake fibrosis. Choyamba, musati mantha. Tiyenera kudziwa zambiri za matenda kuti athe kuthandiza mwana kuthetsa mavuto ake. Nkofunika kukumbukira nthawi iye amakonda.

Matendawa kwambiri zimakhudza thanzi, komanso kumlingo pa maganizo. Choncho, mavuto tingachite pokonzekera (Koma iwo alipo ndipo angamulerere ana athanzi). Ena mpheto ungakhulupiriridwe kuchita ndi mtima wamng'ono. Akatswiri amanena kuti pamene ana sikuti kuphunzira matenda awo, komanso kusamalira okha, kumverera bwino.

Makolo sanaganize yekha polimbana enaake fibrosis, muyenera kulankhula ndi mabanja awo, amene akukumana ndi vuto ofanana. Izo zikhoza kuchitidwa ndi maonekedwe wapadera Internet. Pali kwambiri ndalama, angapemphe thandizo onse maganizo ndi ndalama. Nkofunika kukumbukira kuti matenda amenewa - osati chiweruzo. Anthu ambiri otchuka matenda a majini, koma izi sanasiye iwo bwino moyo. Woimba Gregory Lemarchal, azithunzithunzi wosewera Bob Flanagan (zogwirizana ndi zaka 43) - izi ndi zina mwa zitsanzo chabe za mmene tiyenera kukhalira ndi kukula ndi matenda amenewa. Komanso, mankhwala Kodi chilili: kafukufuku lonse imachitika pa mankhwala jini ya enaake fibrosis mu United States. Koma ngati kupirira ndi maganizo awo kovuta, inu nthawi zonse amafuna thandizo ku zamaganizo a.