ThanziMatenda ndi zokwaniritsa

Ichthyosis khungu: zimayambitsa, zizindikiro, chithandizo

Medicine allocated gulu osiyana matenda, chimene chayambitsa ndi kusintha wosanjikiza zachiphamaso wa khungu pa mlingo chibadwa. Chifukwa chophwanya wa khungu amaloŵamo kusintha zina ndi zimakhala zofanana ndi mamba nsomba. matenda anatengera angasonyeze pa munthu m'badwo uliwonse mutundu, jenda ndi chuma chawo. Ichthyosis tingasonyezere bwino ndipo si kwa wodwala mavuto alionse ndipo akhoza kukhala ndewu ndi kuyambitsa imfa. ichthyosis ndi ichthyosiform khungu matenda ndi mitundu kulemera ndipo mwatsoka, ali ndi ofanana ndi ovuta kuchiza. Ambiri akutsogolera Laboratories zachipatala akulimbikira kuti mwanjira kutsitsa kudwala ndi moyo mosavuta odwala.

ichthyosis Kodi

Nthenda mapangidwe a stratum corneum - ichthyosis. zimayambitsa ndi chifukwa kuvutika mu malamulo majini a kholo limodzi kapena onse - ndicho, mu X-khromozomu. Pali matenda ambiri amene zimapezeka ndi kuyang'ana ngati ichthyosis, koma kwenikweni sizili choncho. Chifukwa mantha kudziwa pa zizindikiro zofanana sikofunika. The matenda enieni angasonyeze yekha katswiri, ndipo ambiri a iwo ofanana ndi matenda khungu bwinobwino anawachiritsa. ichthyosis ndi ichthyosiform matenda khungu ndi mitundu yosiyanasiyana, koma mankhwala ndi mwalamulo ukugawa iwo mu magulu angapo. Dziwani zambiri za aliyense wa iwo - pansipa.

ichthyosis wamba

Amatchedwanso ichthyosis vulgaris, ndi za mtundu wina ambiri. Matendawa kumaonekera ali aang'ono, koma mosiyana mitundu ina, kodi sanaphe ana osaposera 3 months zakubadwa.

The matenda ambiri aukali khalidwe pa kusasitsa kugonana wodwalayo, ndipo pafupifupi 10 zakubadwa. Pamene mahomoni ziziyenda munthu, kubwera ndi kusintha chikhalidwe khungu. Mpumulo amabwera mu chilimwe, koma kuzizira chithunzithunzi matenda ayamba patsogolo. Anyamata ndi atsikana ndi mwayi wofanana angathe matenda. ichthyosis wamba ndi inasamutsidwa kuchoka chonyamulira (kholo limodzi) mwanayo. matenda akuyenda mtima moyo, chikhalidwe akhoza kusintha ndi kuvutika.

Zizindikiro za ichthyosis vulgaris

Ichthyosis vulgaris afika dzina chakuti ankaoneka kudzionetsera. matendawa amakhudza khungu, masaya pamphumi ndi milomo contours kwambiri. Khungu yokutidwa ndi yaing'ono yochitidwa mamba diso zomveka bwino. maonekedwe awo ndi kumaoneka ngati chimanga tirigu, chifukwa nthawi zambiri ngati ichthyosis wa khungu amatchedwa "zipere pityriasis". malo anakhudzidwa sali pansi reddening kapena kutupa, koma khungu amakhala ouma ndipo flaky. Matendawa sikumangotikhudza tsitsi kapena misomali wamkulu wodwala ndipo sanali chifukwa mavuto ambiri.

Nkhope - yekha choyambirira malo malo, nthawi, flaking chikuchitika kwathunthu, koma zakhudza m'madera ena a thupi. Nthawi zambiri bondo ndipo chigongono, m'chiuno ndi kutsikira m'dera kumbuyo, nthawi zina bondo. Izi sikumangotikhudza ichthyosis, mosiyana ndi zinyama zina, groin m'dera ndi motsindika makutu khungu lalikulu. Ndi chikhalidwe cha matenda ndi kukula ndi mawonekedwe a flakes zachilendo khungu ichthyosis anawagawa mitundu ingapo: ichthyosis yosavuta, xeroderma Njoka, singano, wakuda ndi yosalala (pearlescent) ichthyosis.

yokhudzana

Ana ndi achinyamata amavutika kwambiri ichthyosis. Pali zifukwa monga kuyan'anila za ziwalo ndi machitidwe thupi.

  • The mwana pang'onopang'ono kukula kapena kupeza kulemera, zikuwoneka okhota, zolakwika mu chitukuko maganizo.
  • Kupititsa patsogolo katulutsidwe wa sebum ndi thukuta, monga chotsatira - kapangidwe tsitsi wasweka, iwo akhoza kugwera kunja. Nail mbale Akhristuwo, woonda ndi Chimaona.
  • Imachepetsa chitetezo cha m'thupi ndipo chifukwa nthawi zambiri ana amadwala matenda tizilombo ndi yotupa.
  • Kutanganidwa kagayidwe ndipo thupi chithokomiro timadzi.
  • The mafuta magazi likutuluka, yomwe ankatha kuyambitsa matenda a mtima ndi mtima dongosolo.
  • Mukhale "khungu" - chikhalidwe kumene anthu safuna kusiyanitsa zinthu mu mdima.

mavuto onsewa makamaka amamvekera nyengo yozizira. M'pofunika kupereka ulemu wapadera kwa zakudya ndi thanzi. Ndi wofunika mpweya wabwino ndi dzuwa.

Wamba ichthyosis mu mawonekedwe recessive

Matendawa recessive ichthyosis mu mawonekedwe amasonyeza mawonetseredwe wamphamvu wa khungu ukuchoka pa thupi lonse ndi amamangidwa ndi jenda: zowawa fomu iyi yokha oimira wamwamuna. Atsikana kawirikawiri amadwala, koma zonyamulira. Ngati amayi, iwo zimafalitsa matendawa kwa ana ake, kenako kupereka cholowa khromozomu ana awo aakazi. Choncho mukhoza mpaka kalekale.

Kwa atsikana recessive mawonekedwe a matenda chakupha. Zikatero n'zochepa ndi chikhonza kuchitika pokhapokha ngati makolo ake onse akhala kachilombo, ndiye amapereka pathologic X khromozomu mwana wamkazi. Matendawa kwambiri, asungwana awa kawirikawiri kupulumuka.

Zizindikiro za mtundu recessive

Nthawi zambiri anakhudzidwa khungu, tsitsi kupatulira, kusiya, akhoza kubwera dazi wathunthu. Flakes zazikulu wakuda, mosiyana ndi mitundu olaula ndi chodera. Odwala akudwala matenda a ziwalo. Akhoza kukhala matenda fupa ndi retardation maganizo, corneas mitambo, pali milandu khunyu.

Kobadwa nako ichthyosis mu chaukali

Kobadwa nako ichthyosis - ndi kudwala zovuta kwambiri, mwina wofatsa kwambiri kapena. Chiwerengero cha kupulumuka ndi laling'ono kwambiri, ana anaphedwa pasanathe maola angapo pambuyo pa kubadwa. Nthawi zina, mwana amalowerera kupulumutsa. Matendawa mutates mu njira zosiyana, erythroderma, mwachitsanzo. Nthawi zina kwambiri, zimene angatchedwe chozizwitsa, matenda kwathunthu recedes ndi zaka ndi munthu zambiri konse nkhawa.

Zizindikiro za chaukali

Kobadwa nako ichthyosis ana kumaonekera angapo matenda ndi malformations. ana awa amabadwa masiku asanakwane, ndi kulemera otsika kubadwa. Khungu mwana kubwezedwa ndipo akufanana zida, amene amapereka ming'alu ndipo ukutulutsa magazi.

Pa nthawi pamene chitukuko cha khungu mwana wasweka, ziwalo zina, zimakhala ndi ntchofu kupitiriza bwinobwino. Khungu si zotanuka, zikupereka ndi kutembenukira Ufumuyo kwa nsalu kunja. Nkhope ndi thupi lonse mwanayo kwambiri opunduka ndi kutenga maonekedwe zachibadwa.

Chifukwa mlingo mkulu imfa mwa ana chifukwa chakuti nkhani keratin zambiri ndipo chimakakamiza kapena kwathunthu amaononga ziwalo zofunika kwambiri. Newborn sangathe kupuma, kudya, ziwalo ndi zofooka mu chitukuko, amagwirizana ndi matenda. ana awa akutchedwa "Harlequin" ndi matenda - ". Harlequin chizindikiro"

Kobadwa nako ichthyosis wofatsa

Ngati kobadwa nako ichthyosis akufotokozera wofatsa (chosaopsa) mawonekedwe, mwana afika mwayi moyo. Keratinized minofu limakula osati mochuluka monga maonekedwe kwambiri. ziwalo, ngakhale olumala, angathe kugwira ntchito yake yofunika.

Zizindikiro za wofatsa

Ichthyosis ana zingakhudze khungu lonse, kapena zigawo yekha yeniyeni. M'madera ena, khungu amakhala ofiira, edematous palpated pansipa chisindikizo, makamaka m'madera makwinya khungu. m'madera Pathological pa nkhope mwina amaipitsa maonekedwe, kupotoza lids kapena mphuno ndi mkamwa m'deralo. Koma mwayi wa kupulumuka ana amenewa.

Ichthyosis mu "wanzeru" mawonekedwe

Chotero khungu ichthyosis nthawi zina amasokonezeka ndi zoster tsitsi. Iwo akuwonetseredwa mu n'kupita kumene khungu akuyesetsa (bondo, chigongono mafupa). Foci yokutidwa ndi tinatake tozungulira ang'ono amene apitirira ndi lalikulu wofiirira mamba chonyezimira.

kupewa

Ichthyosis - matenda a khungu kuti sangathe kupewedwa, koma n'zotheka kulosera za kubadwa kwa ana ndi matenda. Panali zambiri malo zolelera zomwe kupereka geneticists uphungu. Akatswiri adzakhala kuganizira magawo onse, makamaka ngati banja wamng'ono kapena achibale awo akhala milandu ichthyosis. Chibadwa chingafanane ndi asilikali ndi mavuto angathe matenda kwambiri mwana wosabadwayo ndipo amavomereza za tsogolo la kulera mwanayo. Ngati mavuto n'zambiri, awiri izi zikhoza kukhala analangiza kupereka kubadwa kwa mwana. Mulimonse mmene zinakhalira, kusankha kudzadalira kokha akazi a.

matenda Ichthyosis mu mawonekedwe aakulu - matenda zoopsa kwambiri. imfa khanda pafupifupi 100%. Ngakhale ngati mwana wanu ndi kukhala ndi moyo, ndi chodziwikiratu muyezo wake wa amoyo angatchedwe omasuka. Chotero mwana sangathe kukhala bwinobwino. Iye adzakhala phunziro kwa comorbidities ambiri, chilichonse chimene adzakhala amayambitsa mavuto ululu. okwatirana ayenera kusonyeza udindo ndipo musataye malangizo a akatswiri.

chithandizo

Inu amapezeka ndi "ichthyosis"? Kodi kuchiza matenda? Nawo mankhwala ndi kulamulira zochita za matenda, dermatologists, geneticists, madotolo ndi matenda opatsirana. Mwatsoka, matenda ananena kuti matenda a majini, ndi sikutheka kwathunthu muchisiye izo. Medicine likhoza kukhala ndi khalidwe la moyo wa wodwalayo pa mlingo yoyenera ndiponso aliyense kusokoneza zikamera matenda. Creams ndi zodzola kuti iodzafewa ndipo mankhwala madera anakhudzidwa, odwala adzakakamizika ntchito pamoyo wawo.

matenda ichthyosis ndi zovuta ndi maganizo. Mungafunike wowerenga maganizo, ndi thandizo yofunika mabwenzi apamtima. Kukana anthu sangakhale nkhawa boma kale zovuta munthu. Ana amafunika kulankhulana ndi anzawo. Nkofunika kufotokozera ana kuti matenda si opatsirana ndipo si owopsa kwa iwo.

M'pofunika kukhala chitetezo chokwanira. Mphamvu ayenera kukhala wangwiro. Kuothera dzuwa, koma onetsetsani kuti kupewa kake kakupsa ndi dzuwa ndi kutenthedwa. Kuonetsa akusamba mu madzi nyanja kapena kusamba ndi nyanja mchere. M'pofunika ndi moyo wathanzi ndi pa matenda pang'ono pofuna thandizo kwa madokotala. The matenda pang'ono umalowa mu thupi chofooka, amatha mofulumira kusintha mu matenda khola ndi zosokonezeka.

njira Traditional mankhwala a ichthyosis

Ochiritsa kupereka malangizo kwa unyinji wa anthu amene amadwala wazikang'a khungu. Iwo ali onse osiyana ndi anatanthauza kuti mwanjira kuchepetsa matenda ndi kuchepetsa nkhawa. Komabe, kumbukirani kutsatira malangizo a anthu omwe ali ndi zoyenerera zokayikitsa kuti mankhwala, kusamala ayenera kugwiritsidwa ntchito. Ngati agogo mu msika adzakhala zotopetsa kuzembera inu mankhwala "kwa zilonda ichthyosis Shleymana", limene chikhalidwe kulibe, ndi bwino kusunga ndi "ntchitoyi" kutali. Koma mankhwala palidi ataima malangizo. Ambiri, teas awa ndi malo osambira pa decoction a zitsamba. Pali maphikidwe kwa mafuta kunyumba ofotokoza hydration, zakudya ndi khungu disinfection. Onse anapangidwa kuchokera zosakaniza zachilengedwe ndi kuphika iwo kunyumba n'kosavuta. Mwina mukhoza kusankha okha ochepa ogwira ndi osavuta maphikidwe.

Pamwamba Kufunafuna mankhwala anthu odwala matenda chibadwa, majini ndi zasayansi ntchito m'mayiko ambiri. Tiyeni ndikuyembekeza kuti mankhwala adzapezeka posachedwa, ndipo tidzatha kuchotsa anthu ku matenda ngati zosasangalatsa woopsa.

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