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Kodi Morgagni-Stewart-Morel syndrome?

Syndrome wa Morgagni-Stewart-Morel, chithunzi kusonyezedwa amene Tingaone m'nkhani ino, ali osowa - anthu miliyoni amadwala onse zana yekha ndi forte. Komanso, mu kuchita, akatswiri maso makamaka ndi "makombo" matendawa, chifukwa matenda akufotokozera padera kwa zaka zambiri, ndi zizindikiro imathamanga osiyana. Odwala ndi kuyezedwa osati dokotala patsogolo syndrome kuonekera kwathunthu ndi kudziwa matenda enieni.

Boma kuweruza matenda umalandira, pamene ndipamene pathological inasinthiratu mu thupi. Pambuyo pake, kuthandiza wodwala sizingatheke.

nkhani

Syndrome wa Morgagni-Stewart-Morel wakhala bwinobwino anafotokoza mu 1762, pamene dokotala wodziwa za vutoli Italy Morgagni anatsegula mtembo akazi makumi napeza thickening a mkati mwa mbale mazunzo fupa. Pa nthawi yomweyo, anaona kunenepa ndi thupi amaika tsitsi. Morgagni anapeza zizindikiro za zogwirizana ndipo anafotokoza kuzipenya wake. Kenako, pa osakaniza zizindikiro anaona Morel ndi Stewart anatha kuwonjezera pa cithunzithunzi matenda maonekedwe osiyanasiyana a ubongo ndi maganizo.

matenda Kodi

Morgagni-Stewart-Morel syndrome - matenda amene mazunzo wapezeka hyperostosis mkati fupa mbale, kunenepa ndi chiwerengero cha endocrine ndi kagayidwe kachakudya matenda ena. Matenda a ambiri zimachitika akazi, makamaka patapita zaka makumi anai, koma nthawi zina kuonekera ndipo makumi atatu. Mwa amuna syndrome pafupifupi zimachokeradi, kupatulapo osowa.

Etiology ndi pathogenesis

Disease Morgagni-Stewart-Morel - syndrome, pathogenesis ndi etiology amene ali ndi tanthauzo limodzi. Ena olemba ndikukhulupirira kuti kudwala ndi majini ndi kudzera mwa mtundu autosomal lalikulu. Pali maganizo kuti matendawa Pali kugwirizana ndi X-khromozomu. Panali milandu pamene matenda anavutika mibadwo inayi, ambiri akazi.

Pali milandu akutali maonekedwe syndrome anthu. Koma iwo ayi, ndi sayansi sanayambebe bwino mmene matenda imafalikira kudzera mu mzere wa mwamuna. Ena amakhulupirira kuti matendawa nthawi zambiri m'zimene akazi pa kusintha. Koma deta anapeza pa nthawi, kuika mawu mu funso.

Matendawa akhoza kukhala chifukwa matenda (makamaka sinusitis), neuroinfections komanso zoopsa choipa ubongo. Anapezeka syndrome Morgagni-Stewart-Morel castrates akazi amene opaleshoni. Ena mbali ya matendawa akhoza kupangidwa mankhwala khansa.

Panali milandu pamene matenda anali atazindikira mwa odwala:

  • uterine myoma;
  • sklerokistoz mazira;
  • kulimbikira galactorrhea;
  • maliseche infantilism.

Morgagni-Stewart-Morel syndrome: kudwala

Pamene matenda si thicker mkati mazunzo fupa mbale, koma nthawi zina wapezeka hyperostosis mutu ndi fronto-occipital dera. Pali ambiri kusintha tosaoneka mu zopangitsa za endocrine. Kuwonjezera chiwerengero cha eosinophil ndi basophil maselo. Yambani adenomatous kuchuluka (chithokomiro, adrenal kotekisi ndi T. D.).

zizindikiro

Munthu akapezeka syndrome Morgagni-Stewart-Morel, pali zizindikiro zomwe izo:

  • Odwala amayamba kupeza mutu zonse.
  • Kunenepa, makamaka m'dera m'mimba.
  • Khungu akuzisunga mtundu wabwinobwino, koma nthawi zambiri ndimaoneka pyoderma ndi kulira chikanga.
  • Nthawi zambiri pali kutchulidwa hypertrichosis.
  • Pa khungu amalembedwa pastoznost ayamba pathupi nthambi m'munsi, zikuoneka akrozianoz.
  • Minofu kufooketsa.
  • Pali kusintha mu dongosolo mtima ndi ziwalo kupuma (mtima kukulitsa, pali malankhulidwe ugonthi ndiponso kulephera mtima).
  • Chizolowezi kusokonekera catarrh wa chapamwamba kupuma thirakiti bronchopneumonia.
  • Kusintha zopangitsa endocrine mbali khalidwe nazo. Kusinthana kungakhale kwabwino, kuchuluka kapena utachepa.
  • Zimam'patsa kulolerana amachepetsa. Nthawi zambiri shuga ndi kuonekera.

  • Posasangalala msambo. Mimba, nthawi imeneyi alili chatsitsa.
  • Pali matenda mantha ndi maganizo. Iwo zimapezeka mu mawonekedwe a lability maganizo, irritability, kusowa tulo ndi chizolowezi maganizo.
  • Internal mazunzo hyperostosis mbale kawirikawiri unakhuthala mafupa achigaza. Nthawi zina, ngakhale kuwonjezera kukula kwa chishalo Turkey.

matenda

Morgagni-Stewart-Morel syndrome akhoza kuchita pa thupi m'njira zosiyanasiyana. Kawirikawiri izo zimatengera mlingo wa kunenepa. Kutchulidwa amakhudza kwambiri pa moyo amayembekezeka:

  • ntchito ya mtima ndi zovuta;
  • chifukwa kudzikundikira mafuta zimachitika myocardium ndi pericardium;
  • udindo wa chifundamtima;
  • magazi, ndi osakaniza atherosclerosis ndi matenda oopsa osauka mtima kulephera, umene ndi chifukwa cha kulumala;
  • ngati wodwala ndi matendawa ali ndi matenda a shuga, ndiye iwo amayamba ndi matenda kagayidwe kachakudya, imbaenda osati kuti kuchepa mu dzuwa, komanso amachepetsa moyo zaka zambiri.

chithandizo

Kodi zingatheke kuthetsa vuto la Morgagni-Stewart-Morel? Kuchiza matenda ndi makamaka zakudya zofanana shuga assignable ndi kunenepa. Chakudya ayenera kukhala otsika-kalori, mkulu-mapuloteni, mavitamini ndi mchere salt. The zakudya amachepetsa chiwerengero cha chakudya mafuta. Zakudya Baranov akapatsidwa makamaka.

Komanso, mankhwala ikuchitika kutikita ndipo anatumizidwa ku akamachita maphunziro thupi kuchepetsa minofu kufooka ndi kusintha makope zotumphukira. Ngati wodwalayo mtima kulephera, chithandizo cha matenda unachitikira okodzetsa kardiopreparatami ndi T D..

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