ThanziMatenda ndi zokwaniritsa

Zokhudza zonse vasculitis: zizindikiro ndi mankhwala. Vasculitis - chiyani matenda?

Vasculitis - kodi matenda ndi mmene zovuta bwanji thupi mu chikhalidwe ichi?

matenda mtima

Mitsempha chifukwa zinthu zosiyanasiyana oipa akhoza kutaya ntchito zawo, ndipo izi zimakhudza mmene chamoyo wonse.

Zokhudza zonse vasculitis - matenda amene amagwirizana ndi nthenda makoma mtima. Pa gawo lino muli mitundu yambiri ya matenda.

Mitundu ya matenda zokhudza zonse

Kudziwika mitundu ya kusintha mtima pathological:

  1. Kugonjetsedwa kwa zigawo munthu wa mitsempha sing'anga kapena ang'ono-likungosonyeza otchedwa periarthritis nodosa.
  2. Matenda imagwira makamaka mitsempha ndi mitsempha wa kapepalako kupuma ndi mapapo, impso ndi pamenepo pokha, limanenedwa ngati granulomatosis Wegener a.
  3. Zokhudza zonse vasculitis, amene Zizindikiro zimasonyeza kudwala ziwiya waukulu wa thupi (nthawi zambiri - mitsempha mutu), wotchedwa chimphona selo zosatha arteritis.
  4. njira yotupa mu mitsempha lalikulu ndi msempha limanenedwa ngati matenda Takayasu, kapena aortoarteriit nonspecific.
  5. Monga za kudwala kwa mitsempha mtundu akulu, ndiye matenda chimatanthauza obliterans thromboangiitis.
  6. matenda zokhudza zonse zomwe limodzi ndi zizindikiro monga stomatitis, ndi chotupa zimakhala mkamwa ndi mucosa maliseche, komanso kusintha mu diso umatchedwa "syndrome Behcet Mulungu."
  7. Matupi awo sagwirizana vasculitis.

Onse mitundu pamwamba imakhudzana ndi zimayambitsa ena kuti amakwiya kusintha mu Mitsempha ndi kuphwanya ntchito zawo.

Zimayambitsa matenda

Kudziwa patsogolo chithandizo zomveka ndi zodzitetezera, m'pofunika kudziwa chimene chimachititsa izi kapena kuti kusintha pathological ziwiya. Zikatero, zokhudza zonse vasculitis angakhale ndi zotsatira zabwino wodwalayo.

Bwinobwino anaphunzira zinthu zonse zoyambitsa matenda, koma zifukwa izo kapadera:

  1. Zokhudza zonse vasculitis monga anachita thupi kugwiritsa ntchito mankhwala ena. kusintha Pathological makoma chotengera akhoza zoyambitsa matenda enaake amene akhala ananyoza chithandizo.
  2. Zokhudza zonse vasculitis monga vuto la matenda ena opatsirana aukali kuti akhala anasamutsidwa.
  3. Mitsempha akhoza adzawonongedwa pa matenda monga zotakasika nyamakazi, zokhudza zonse lupus erythematosus, njira yotupa mu chithokomiro, ndi aakulu pathologies autoimmune, syndrome Schwartz-Jampel, ndi zina glomerulonephritis.

Mfundo zonsezi kudziwa vasculitis zokhudza zonse. Zizindikiro ndi mankhwala a matenda si nthawi zonse zogwirizana, chifukwa ena mwa maonekedwe a matenda ali mu mawonekedwe zobisika, pamene ena, Tikawonetsetsa ndi kukankhira kusaina matenda cholakwika.

Kodi chimachitika m'thupi? pathogenesis

The kudwala a dongosolo mtima zikuphatikizapo kusintha makhalidwe oipa thupi, amene amaoneka pamisinkhu yosiyanasiyana matenda. Mfundo ndi kuti nsupa analanda yotupa ndondomeko ndi chiwonongeko wotsatira wa nyumba yawo.

Mtundu uliwonse wa vasculitis anapereka chimaposa ndi makhalidwe yake.

Kodi kusintha limodzi ndi mtundu uliwonse?

  1. Pamene syndrome Behcet anati zizindikiro mu M'mimbamo m'kamwa, makamaka stomatitis, amene atuluka ndi musabise. Gawo lachiwiri la chizindikiro angatchedwe zilonda mu scrotum amuna ndi akazi - mu nyini ndi akumaliseche. Komanso mucosa, mtundu wa vasculitis amakhala osiyana amakhudza eyeballs.
  2. obliterans Thromboangiitis limodzi ndi madandaulo a anthu odwala, chitukuko cha kupunduka kapena dzanzi mwadzidzidzi manja.
  3. Aortoarteriit amapereka zotsatira nonspecific monga kupweteka m'munsi ndi chapamwamba malekezero, kupweteka kwa msana, lopatsidwa m'mimba, komanso kukomoka ndi matenda okhudzana ndi maso.

Mitundu ina, malingana mwamphamvu, ndi pafupifupi zizindikiro zomwezo, koma amafuna munthu njira mankhwala.

symptomatic chithunzi

Symptomatology matenda mtima akhoza kusintha chithunzi chanu, malingana ndi zimene ndondomeko kutanthauzira ndi pathologies kuti atsagane nawo.

Vasculitis chifukwa totupa, ndi zisokonezo pathological mu wamanjenje dongosolo kumaphatikizapo kuchuluka tilinazo, zomwe zingasiyane hypersensitivity kuti tilinazo otsika kapena kusapezeka kwake kwathunthu.

Pamene magazi ziwiya ubongo, kumeneko kumachitika sitiroko ndi matenda a mtima. Matupi awo sagwirizana vasculitis kuwawonetsera monga mmene ndi matupi awo sagwirizana anachita nzothandiza a.

Zizindikiro za kudwala mtima

Pali zina zizindikiro zosonyeza aliwonse vasculitis ndi:

  • tsankho kapena wathunthu kukana kudya;
  • kufooka chamoyo lomwe limapezeka popanda chifukwa ndi limodzi mwa mphwayi;
  • kutopa mofulumira, mwakuthupi komanso makhalidwe;
  • okwera thupi kutentha - otsika kalasi, nthawi zina chimabwera kwa febrile;
  • wotumbululuka khungu, kugwirizana ndi kuphwanya makope ambiri mu thupi.

kwa vasculitis zokhudza zonse zimene wina? Kodi matenda ndi momwe kuti tipewe, mungazipeze pa zina wamba. Mwachitsanzo, mtundu nodular wa vasculitis akuwonetseredwa minofu kupweteka onse pa thupi. Ululu chimafikira kwa m'mimba, imfayo kuwonda, matenda m'mimba, kusanza, ndipo monga Motero, mavuto a m'maganizo.

granulomatosis Wegner a, amakwiya matenda a m'mphuno, kapena yeniyeni, pa chifuwa chake - mafinya magazi ndi ntchofu. njira anam'peza angayambe pa amphuno mucosa. Ndiye chifuwa zikachitika, chifuwa ululu, kufupika kwa mpweya, kulephera impso ndi ena.

zotupa

Pamene njira pathological m'zotengera chifukwa sayanjana, ndiye mtundu wa vasculitis otchedwa khungu. Kodi khungu vasculitis?

Umaimiridwa ndi matenda ali mitundu yambiri ya otaya:

  • woyamba mtundu - nodosa necrotic kapena Werther-Dyumlinga anaonetsa malo dermal pa khungu ndi zofiirira mthunzi bluish;
  • chachiwiri - matupi awo sagwirizana arteriollit Ruiter, amene amadera lililonse eritrematoznymi totupa pakhungu, komanso crusts hemorrhagic, zilonda, erosions ndi necrosis wotsatira.

Matenda a matenda zokhudza zonse mtima

Kusankha njira yodziwira zikhazikitsidwe mawonetseredwe kunja vasculitis, koma kudziwa mtundu zobisika chochita zinthu zina pa kafukufukuyu.

Kuyamba wodwala angathe ayenera kutenga magazi kudziwa kusintha mwa iye. Pamene zizindikiro kachulukidwe wa hemoglobin ndi kwambiri poyerekeza wabwinobwino, umasonyeza chiyambi cha njira magazi ochepa thupi - vuto lalikulu kudwala mtima.

Kawirikawiri, koma zimachitika pamene matenda "zokhudza zonse vasculitis" aikidwa pa maziko a kusanthula mkodzo, ngati kudziwa maselo ofiira ndi maselo oyera.

The chachiwiri zofufuza mtengo, koma si zofunika kwenikweni kwa matenda, ndi biopsy. Kuti zimenezi zitheke, wodwalayo kufufuza tosaoneka ayenera kutenga mbali ya chotengera minofu.

Zokhudza zonse vasculitis. Zizindikiro ndi Chithandizo

Malinga kaya ndi matupi awo sagwirizana vasculitis kapena chithandizo sekondale Kwalamulidwa payekha, ndipo imatsogoleredwa osati chithandizo cha matenda enaake, komanso kubwezeretsa kwa thupi lonse, amene anali lowonongeka ku maziko a kudwala mtima.

Cholinga cha njira ndi kuwonongedwa kwathunthu kwa zizindikiro za matendawo, normalization Mitsempha ndi kufalitsidwa.

Mankhwala oyenera zokhudza zonse vasculitis:

  • corticosteroid mankhwala;
  • chemotherapeutic wothandizila;
  • immunosuppressants.

Pamene amtopola vasculitis zofunika kuchita odwala mwakayakaya ndi mankhwala. Izi ndi zofunika mu nkhani ya wonongeka ziwalo zofunika monga mtima, chiwindi, m'mapapo, impso. Pankhaniyi, ndi kuwatsitsimula mtima akutsatiridwa ndi mankhwala symptomatic.

khungu vasculitis anafunika kuchitira ndi outpatient kapena ali kuchipatala, malingana progressiveness za ndondomeko pathological. Mogwira matenda adzakhala mmene kwakukulu akonzere malo a matenda amene amapezeka kale mu gawo aakulu.

Wodwala ayenera kutsata ndi bedi zina ndi kutenga mankhwala zotsatirazi:

  • mankhwala, kuphatikizapo mankhwala ochiza vasculitis ndi "Promethazine", "ndi diphenhydramine", "Fenkarol";
  • Kukonzekera kashiamu microelement - 10% kashiamu mankhwala enaake jekeseni kapena njira gluconate;
  • rutin, ascorbic acid.

Pamene inefficiency ntchito mankhwala chipangizo kwambiri ntchito yokonzekera m'thupi monga mankhwala "prednisolone" ndi "Dexamethasone".

Pamene matenda limodzi ndi chilonda ndi njira necrotic, chithandizo chikuphatikizapo ntchito apakhungu a mafuta glucocorticoid (mafuta "Boron-naftalan" "methyluracyl" ndi ena), kukonzekera epitelioplasticheskie.

Mu nthawi yaitali, koma sizithandiza chithandizo m'njira ndi kugwiritsa ntchito ndalama angiotroficheskih. mankhwala "dobesilate kashiamu", "ksantinola nicotinate" ndi ena.

ndi madokotala ananena zawo za matenda chiyani?

Kuti madokotala ananena zawo zimadalira mtundu wa vasculitis ndi kukula kwa matendawa. matenda oyambirira ndi mankhwala mwamsanga akhoza kwambiri kutalikitsa moyo wa wodwalayo. Nkofunika kuti matenda ndi kukhala ndi mulingo woyenera chithandizo chakudya. Muyenera molondola kusankha mankhwala ndi mlingo pofuna kupewa mavuto ndi zotsatira zake zoyipa.

N'zosatheka kuneneratu zotsatira za matenda monga zokhudza zonse vasculitis. Mankhwala ayenera kupitiriza moyo. Childs, matenda ndi aakulu, ndipo nthawi exacerbation akutsatiridwa ndi nthawi ya chikhululukiro. Disease vasculitis zambiri osati kwathunthu anawachiritsa. Munthu nthawi zonse amakakamizidwa kukaona dotolo ndi kulamulira zizindikiro.

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