Thanzi, Matenda ndi zokwaniritsa
ALS syndrome. Amyotrophic lateral sclerosis: Chithandizo
Mu 1869 ku French zamaganizo Charcot anapanga kufotokoza molondola matenda ndiyo amyotrophic lateral sclerosis.
ndi matenda Kodi
Ndi chitukuko cha matenda ndi alibe wa manyuroni zotumphukira wa dongosolo chapakati mantha a njira yaikulu. Komabe, ena zinthu m'malo mwa glia. Pyramidal mtengo zambiri zimakhudza wamphamvu kwambiri kuposa momwe izo zinaliri mu zipilala zam'mbali. Choncho epithet - mbali. Koma manyuroni zotumphukira, izo kwambiri anakhudzidwa m'dera la nyanga zapambuyo. N'chifukwa chake matenda limodzi ndi epithet wina - amyotrophic. Pa dzina chomwecho molondola imasonyeza chimodzi cha zizindikiro matenda a matenda - minofu ya manja. ALS syndrome si nthenda yoopsa. Dziwani kuti dzina matenda Charcot, kwambiri akuganizira zochititsa khalidwe: zizindikiro za pyramidal mtengo uli ndime mbali, pamodzi ndi minofu ya manja.
zizindikiro
Masiku ano, anthu ambiri amakakamizika kukhala ndi matenda matenda a ALS. Zizindikiro za matenda osiyanasiyana ndithu. Dziwani kuti zizindikiro zosonyeza kuti matendawo ali pafupifupi ayi. ALS akufotokozera payekha. Mu magawo oyambirira, pali zizindikiro amatithandiza kudziwa chitukuko cha matenda.
- Movement matenda. Wodwala akuyamba nthawi chokhumudwitsa, kusiya zinthu ndi kugwa chifukwa cha kufooka ndi tsankho minofu ya manja. Nthawi zina, zofewa minofu monga dzanzi.
- Kulankhula matenda.
- Minofu omangana. Nthawi zambiri zodabwitsazi amapezeka mu ng'ombe ndi.
- Fasciculations - pang'ono kukokana kwa minofu. Nthawi zambiri zodabwitsazi amatchedwa "tokhala tsekwe." Fasciculations limapezeka kawirikawiri manja a.
- Tsankho Amowabu manja a zimakhala minofu mapazi ndi manja. Makamaka zambiri njira kuti ayamba m'dera la lamba phewa: clavicle, masamba phewa ndi mapewa.
ALS syndrome akufotokozera uliwonse munthu mosiyana. matenda ndi zovuta oterewa mu magawo oyambirira. Ngati munthu ali ndi zizindikiro za amyotrophic lateral sclerosis, koma matenda zikutsimikiziridwa, wodwala akhoza kudwala matenda wina kwathunthu.
Zizindikiro zina za ALS
syndrome ALS amakhala ndi kupita patsogolo. M'mawu ena, manja minofu minofu, ndi kufooka pamwambapa ndi nakweza. Ngati munthu movutikira mabatani a, ndiye pamapeto pake basi sangathe kuchita izo konse. Izi imakhudzanso maluso ena.
Pang'onopang'ono, mtima wotaya luso kuyenda. Poyamba angafunike sasinthasintha zonse, ndi m'tsogolo - wilutcheya. Komanso, minofu wofooka sizingathe kuthandiza mutu wodwalayo mu malo. Nthawi zonse kugwa pa chifuwa. Ngati matenda chidzawavindikira akatumba onse a thupi, ndiye munthu sangathe kudzuka pabedi kwa nthawi yaitali kukhala mu malo atakhala, komanso falitsani uku.
Koma mawu, palinso vuto. Wodwala pang'onopang'ono akufotokozera syndrome ALS. Zizindikiro za matenda angakhale osiyana kwambiri. Pa siteji koyamba wodwala wayamba kunena "mphuno". Mawu ake wayamba zochepa osiyana. Chifukwa, izo zikhoza kutha palimodzi. Ngakhale odwala ambiri kusunga luso la kulankhula, mpaka mapeto a moyo wake.
mavuto ena
Ngati matenda wapangidwa ndi matenda - syndrome ALS, achibale a munthu wodwalayo ayenera kukonzekera mavuto aakulu. Kusiyapo mfundo munthu kuti pafupifupi linasiiratu amatha mavuto ake anayamba chakudya. Nthawi zina, mwina kuyamba salivation. zodabwitsazi kumathandizanso kwambiri za mavuto, ndipo ndi woopsa kwambiri. Inde, pa chakudya wodwala kumeza malovu lalikulu zedi. Panthawi ina mungafunike zakudya enteral.
Pang'onopang'ono pali matenda kugwirizana ndi ntchito ya dongosolo kupuma. Chifukwa cha ichi, kupuma kulephera angayambe. Chotero chapakati mantha dongosolo matenda kubweretsa mavuto ambiri. Nthawi zambiri, odwala ndi mutu ndi dyspnea. Nthawi zambiri anthu ndi ALS amadwala malubwelubwe. Pali nthawi pamene, chifukwa cha kusowa oxygen kuyerekezera zinthu m'maganizo wodwalayo, komanso amakhala disorientation.
Chifukwa pali amyotrophic lateral sclerosis
clinicians ambiri amaona matenda monga ndondomeko osachiritsika. Komabe, zimachititsa woona wa amyotrophic lateral sclerosis akadali osadziwika. Akatswiri ena amakhulupirira kuti matenda ndi matenda amene amayamba ndi mavairasi fyuluta. ALS syndrome ndi matenda n'chosoŵa kuti wayamba kukhala anthu zaka 50.
Koma madokotala zinachitikira ndithu, iwo amakonda kugawanitsa matenda onse organic wa chingwe msana ndi akakufunsani dongosolo. Koma amyotrophic lateral sclerosis, apa zingamvekere yekha galimoto, koma kukhala tcheru mwangwiro bwinobwino. Chifukwa, maphunziro histopathological tapangidwa ena kusinthidwa kwa lingaliro m'chimake a zotupa zokhudza zonse.
Kotero kufotokoza chitukuko cha ichi kapena kuti matenda a ubongo ndi msana? Zikuoneka pansi zina matenda zokhudza zonse kumatengera zifukwa zingapo.
- Special kuyandikana poizoni kapena HIV ndi nyumba zenizeni mitsempha. Ndipo n'zotheka ndithu. Pambuyo poizoni ndi makhalidwe osiyana kwambiri mankhwala. Komanso, chapakati mantha dongosolo ili kutali ndi yunifolomu pa nkhani imeneyi. Mwina ndicho bodza amachititsa amyotrophic lateral sclerosis?
- Komanso, matenda angayambe chifukwa cha kulunjika mwa kundipatsako magazi kuti mbali zina za mantha dongosolo anthu.
- chifukwa angathe kutumikira monga makamaka makope lymph mu njira ya msana ndi likvoobrascheniya mu CNS.
Kotero, n'chifukwa chiyani ALS syndrome? zifukwa adakali sakudziwika. Ndipo asayansi padziko lonse yekha amanena.
matenda a matenda
Nthawi zambiri matenda a amyotrophic lateral sclerosis amachititsa mavuto ena. Ndipotu, kusintha osiyana matenda a madzimadzi cerebrospinal, etiology, pamaso neyrosifiliticheskih nthawi zambiri zizindikiro pupillary. Oterewa syndrome ALS zovuta zifukwa zingapo.
- Izi si matenda osowa.
- Aliyense matenda amachititsa munthu m'njira zambiri. Pankhaniyi, zizindikiro zofanana osati kwambiri.
- Zizindikiro zoyambirira za ALS akhale wachete, mwachitsanzo, pang'ono elongated kulankhula, clumsiness m'manja mwa clumsiness. Mu zizindikiro izi kutchulidwa mwina chifukwa matenda ena.
Komabe, matenda a amyotrophic lateral sclerosis, dziŵani kuti matenda ambiri zimachitika ndi kuwonongeka kusankha kwa nyumba galimoto. Pa matenda a ALS moleza mtima kubva pakhosi, komanso mapuloteni-selo dissociation mowa, chipika pa myelogram ndi imfa tilinazo.
Ngati dotolo anayamba kuganiza kuti azichita wodwalayo katswiriyu ndi. Ndipo pambuyo kuti mungafunike kukumana mndandanda wa mayesero matenda.
ALS chithandizo
Monga tanenera kale, ALS syndrome - matenda osachiritsika. Choncho, dziko sichinafike mankhwala a matenda. Komabe, pali Zida zogwiritsira kuti amakulolani kuthetsa zizindikiro. Mwachitsanzo, ku Ulaya ndi ku United States ntchito "Riluzole" mankhwala. Ichi ndi mankhwala koyamba ndiponso kuti wakhala naye. Komabe, mu dziko lathu, mankhwala silinakwaniritsidwe m'kaundula. Khalirani mwalamulo dokotala sangathe. Tikumbukenso kuti chida ichi si kuthetseratu nthendayi. Komabe, ali zingamvekere moyo amayembekezeka odwala ndi matenda a ALS. Izi mankhwala alipo mapiritsi. Tengani izo kangapo patsiku. Pamaso ntchito, ayenera bwinobwino phukusi ukukamba.
Kodi "Riluzole"
Pamene kufala kwa zikhumbo za mitsempha adzamasulidwa glutamate. mankhwala ndi mtundu mankhwala chapakati mantha dongosolo. Mankhwala "Riluzole" amachepetsa chiwerengero cha glutamate. Kafukufuku wasonyeza kuti overabundance zinthu zimenezi zikhoza kuwonongeka kwa manyuroni a ubongo ndi msana.
Matenda mayesero mankhwala anasonyezanso kuti odwala amene amalandira amatanthauza "Riluzole" moyo wautali kuposa ena. Komabe, moyo wawo amayembekezeka chawonjezeka ndi za 3 miyezi (poyerekeza ndi anthu amene anatenga placebo).
Antioxidants ndi matenda
Popeza zimayambitsa amyotrophic lateral sclerosis sanayambebe anaika, ndipo palibe mankhwala matenda. Asayansi akukhulupirira kuti anthu odwala matenda ALS, ndi sitichedwa mavuto ankafuna kusintha zinthu mopitirira ufulu. M'zaka zaposachedwapa, tinayamba kuchita maphunziro enieni umalimbana akudzizindikiritsa efficiencies onse operekedwa ndi thupi chifukwa cha supplementation ndi antioxidants mu zikuchokera. Patsogolo ntchito mankhwala ayenera kukhala mogwirizana ndi katswiri wa.
Antioxidants ali kalasi osiyana zakudya zimene zimathandiza thupi la munthu kuteteza mitundu yonse ya kuwonongeka ndi ufulu ankafuna kusintha zinthu mopitirira. Komabe, ena zowonjezera amene kale mayesero matenda, tsoka, sanapereke kuyembekezera ubwino. Mwatsoka, matenda ena a dongosolo chapakati mantha kuchiza sangathe. Kodi mungakonde pansiwa.
mankhwala concomitant
mankhwala Concomitant akhoza kwambiri moyo mosavuta amene aona syndrome ALS. Chithandizo cha matendawa - njira motalika kokwanira. Choncho n'kofunika osati mankhwala a matenda chachikulu, komanso zizindikiro kugwirizana. Akatswiri akukhulupirira, kuti amalola okwana zosangalatsa, osachepera yochepa kuyiwala za mantha ndi kuchepetsa nkhawa.
Kumasuka minofu ya wodwala, n'zotheka ntchito reflexology, aromatherapy ndi kutikita. ndondomeko izi matenda kufalitsa lymph ndi magazi, komanso kamakhala kuchotsa ululu. Ndipotu khalidwe lawo ndi kukondoweza amapha amkati ululu ndi endorphins. Komabe, kuphwanya chapakati mantha dongosolo amafuna munthu njira. Chotero, inu amfunsefunse ndi katswiri musanayambe njira za kayendetsedwe.
pomaliza
Pakali pano, pali matenda ambiri osachiritsika. Ndi kwa nkhawa ndi matenda ALS. Photo odwala amyotrophic lateral sclerosis chabe Inabuka mantha. anthu awa waponya ndi mavuto ambiri, koma ngakhale chirichonse, iwo moyo. Kumene, kwathunthu kuchotsa matenda si zotheka, koma pali njira zambiri kuthetsa ena mwa zizindikiro. Chinthu chachikulu kukumbukira kuti munthuyo akudwala vuto la ALS, thandizo ndi kuwayang'anira nthaŵi zonse. Ngati mulibe luso lamanja, mukhoza kupempha thandizo kwa ena akatswiri ndi physiotherapists.
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