Lefgrena syndrome: Zoyambitsa, mbali matenda, mankhwala, kupewa

matenda zokhudza zonse nthawizonse zakhala ziri chinsinsi kwa dziko zachipatala. Limodzi ndi sarcoidosis, limene sayesedwa wolungama pa etiology ndi kuonetsedwa mu mawonekedwe a kutupa kwa minofu connective ziwalo zosiyanasiyana ndipo zimakhala ndi mapangidwe granulomas. Lefgrena syndrome - chapadera sarcoidosis okhudza khungu, intrasternal lymph mfundo ndi mafupa.

zimayambitsa

The pathogenesis ndi chitukuko cha ayankhe autoimmune. The chitetezo cha m'thupi n'zimene, ndi maselo oyera anayamba kugunda wathanzi maselo m'mapapo, mfundo ndi khungu.

Lefgrena syndrome zambiri akufotokozera mu atsikana (zaka 20-35). Ana zambiri iwo kudwala. Lefgrena matenda ayamba bwinobwino, ndiyeno pang'onopang'ono mawonetseredwe matenda mwina okha chichitike. Nthawi zambiri, pali njira yabwino matendawa.

Kuwonjezera chiphunzitso tizilombo toyambitsa chitukuko cha sarcoidosis, palinso kukhulupirira kuti matenda akufotokozera anthu nthawi yaitali kukhudzana ndi mankhwala oyaka m'mafakitale. Muyenera asataye, ndi chinthu cholowa. N'chifukwa chake polyetiological sarcoidosis ndi matenda autoimmune.

mawonetseredwe matenda

Lefgrena syndrome mu sarcoidosis kuwawonetsera polisimptomno. Matenda mawonetseredwe kuyamba bwinobwino. munthuyo ali erythema nodosum pa thupi, ali ndi chizolowezi kufalikira ku malekezero, kumbuyo, m'mimba ndi khosi. Mfundo ndi mawonekedwe chowulungika, awiri awo akhoza kufika mpaka 6 masentimita. Tikumbukenso kuti m'malo mapangidwe erythema zimachokeradi necrosis.

Chiwonetsero chachikulu imatengedwa kuti ndi kugonjetsedwa kwa bronchial ndi tracheal zopangitsa. Ichi chikuimira ngozi yaikulu wodwalayo:

• chifuwa;
• zina kuchuluka kutentha thupi;
• kudwala;
• pali usiku Thukuta;
• Kuwonjezeka khalidwe tulo;
• kuwonda amapezeka;
• munthu amakhala ndi nkhawa.

Kenako Lefgrena syndrome amakhala ndi zotupa za malo. Iwo amakhala opweteka edematous ndi kuyenda chatsitsa. Mwachikulu, munthu taonani kutupa kwa mwanabele mu khosi ndi m'khwapa lapansi.

Kodi matenda?

syndrome Lefgrena udzakhazikitsidwe pa maziko a diagnostics zasayansi ndi Kupenda dokotala wodwalayo. Erythema nodosum masewero zofunika Kupeza Vuto mawonekedwe sarcoidosis. Komabe, dokotala ayenera siyanitsa ndi matenda TB kapena matenda dermatovenereological.

MAGAZI Laboratory adzakusonyezani:

• kuwonjezera ESR;
• leukocytosis;
• maonekedwe a Popanga madzi a gamma globulin.

Pa X-ray chithunzi Tingaone khalidwe zikuluzikulu lymph mfundo, komanso madipoziti fibrous. Izi zimathandiza kuonetsetsa pa nkhani ya matenda a m'mapapo.

Ofooka anafotokoza mu mawonekedwe kumafuna bronchoscopy ndi biopsy. Pamene kuphunzira minofu m'mapapo sangathe kuona khalidwe histological Kapangidwe ka sarcoidosis: kupeza zinthu granulomas epithelioid.

Kulosera tsogolo la matenda ndi mavuto a matenda

Payekha umayenda syndrome Lefgrena. nthawi yaitali bwanji ndi zimene ali Zoneneratu angalankhule okha i ena. Amadziwika kuti akulu munthu, kuti madokotala ananena zawo osauka. Ngati mulibe ntchito nthawi kuwona dotolo, matendawa anachedwa ndipo umalumikizana ndi mavuto:

• bronchial kutsekeka;
• kupuma insufficiency;
• chitukuko cha "mtima m'mapapo mwanga";
• ndiko kumayambitsa;
• ndi bakiteriya zomera.

Kupuma kulephera akufotokozera pambuyo kutsekeka bronchial. alili pang'ono ndi pang'ono chatsika monga mapapo anayamba m'malo ndi minofu connective, ndondomeko akhoza kusiya zokha patapita zaka 1-2.

Pang'onopang'ono, mtima akuyamba kuwonjezera chifukwa chosowa mpweya magazi. Koma sitiyenera kunyalanyaza pempho kuchipatala chifukwa tsopano Lefgrena syndrome ndi mankhwala.

chithandizo

Mwatsoka, Medco sangathe kwathunthu kuchiza sarcoidosis, kuyambira etiology ake samadziwika kwathunthu. Koma madokotala mankhwala mankhwala apadera amene akhoza kulepheretsanso chitukuko, kuwunika syndrome Lefgrena. Chithandizo imayamba ndi kopita steroidal mankhwala odana ndi yotupa kwa chitetezo chokwanira otsika. Komanso Kwalamulidwa vitamini maofesi, antioxidants, immunosuppressants.

The njira ya mankhwala kumatenga pafupifupi miyezi 8. Izi zidalira pa makhalidwe munthu wa chitetezo cha m'thupi. Imalimbikitsa kuvomerezedwa zachipatala kukayezedwa odwala dokotala pulmunologom, Choncho iwo kumatenga zaka 5.

Kodi kupewa?

Pofuna kupewa chitukuko cha sarcoidosis, ayambe kusamalira moyo wawo. Chakudya ayenera kukhala moyenera, akupanga mafuta, mapuloteni, chakudya mu chiŵerengero akadakwanitsira.

Anthu predisposed kuti sarcoidosis, ayenera kusiya kusuta, kukhudzana ndi mwamakani mankhwala zinthu.